Erschienen in:
22.04.2020 | Case Based Review
Self-healing juvenile cutaneous mucinosis, a sclerodermoid disorder simulating juvenile dermatomyositis: a case-based review
verfasst von:
Anuradha Bishnoi, Ankur Kumar Jindal, Gummadi Anjani, Pratap Kumar Patra, Debajyoti Chatterjee, Keshavamurthy Vinay, Amrinder J. Kanwar, Sunil Dogra, Surjit Singh
Erschienen in:
Rheumatology International
|
Ausgabe 11/2020
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Abstract
Self-healing juvenile cutaneous mucinosis (SHJCM) is a rare childhood disease with characteristic cutaneous and rheumatic manifestations. Cutaneous manifestations include a combination of nodules affecting peri-articular (especially interphalangeal joints) and head and neck areas; and linearly arranged ivory white papules over an erythematous indurated skin. Despite a benign course, an abrupt onset of symptoms with extensive cutaneous involvement often leads to parental anxiety, overenthusiastic evaluation and sometimes aggressive treatment. A peculiar cutaneous distribution in SHJCM including nodular lesions and periorbital edema, arthritis and arthralgia in a few cases, may simulate juvenile dermatomyositis. It is, therefore, important for dermatologists and pediatricians to be aware of this entity. In this report, we describe two cases of SHJCM and briefly review similarly reported cases in children.