Ausgabe 4/2017
Inhalt (13 Artikel)
Low IgA and IgM Is Associated with a Higher Prevalence of Bronchiectasis in Primary Antibody Deficiency
John P. Hodkinson, Catherine Bangs, Andrea Wartenberg-Demand, Artur Bauhofer, Patrick Langohr, Matthew S. Buckland, David Guzman, Patrick F. K. Yong, Sorena Kiani-Alikhan
Erratum to: Low IgA and IgM is Associated with a Higher Prevalence of Bronchiectasis in Primary Antibody Deficiency
John P. Hodkinson, Catherine Bangs, Andrea Wartenberg-Demand, Artur Bauhofer, Patrick Langohr, Matthew S. Buckland, David Guzman, Patrick F. K. Yong, Sorena Kiani-Alikhan
Severe Aspergillus Pneumonia and Pulmonary Artery Hypertension in a Child with Autosomal Recessive Chronic Granulomatous Disease and Selective IgA Deficiency
Ankur K. Jindal, Amit Rawat, Deepti Suri, Madhubala Sharma, Jitendra K. Shandilya, Shubham Goel, Kushaljit S. Sodhi, Surjit Singh
First Case of X-Linked Moesin Deficiency Identified After Newborn Screening for SCID
Ottavia M. Delmonte, Catherine M. Biggs, Anthony Hayward, Anne M. Comeau, Hye Sun Kuehn, Sergio D. Rosenzweig, Luigi D. Notarangelo
Placental Transfer of Canakinumab in a Patient with Muckle-Wells Syndrome
Makiko Egawa, Kohsuke Imai, Masaaki Mori, Naoyuki Miyasaka, Tetsuo Kubota
Paecilomyces formosus Infection in an Adult Patient with Undiagnosed Chronic Granulomatous Disease
Jalal Heshmatnia, Majid Marjani, Seyed Alireza Mahdaviani, Parvaneh Adimi, Mihan Pourabdollah, Payam Tabarsi, Fereshte Mahdavi, Hamidreza Jamaati, Ian M. Adcock, Johan Garssen, Aliakbar Velayati, Davood Mansouri, Esmaeil Mortaz
Persistent Impairment of T-Cell Regeneration in a Patient with Activated PI3K δ Syndrome
Fumihiro Goto, Toru Uchiyama, Yumiko Nakazawa, Kohsuke Imai, Toshinao Kawai, Masafumi Onodera
How We Manage Adenosine Deaminase-Deficient Severe Combined Immune Deficiency (ADA SCID)
Donald B. Kohn, H. Bobby Gaspar
Poikiloderma with Neutropenia in Morocco: a Report of Four Cases
Ayoub Aglaguel, Houria Abdelghaffar, Fatima Ailal, Norddine Habti, Sebastian Hesse, Naschla Kohistani, Christoph Klein, Ahmed Aziz Bousfiha
Immunodeficiencies Associated with Abnormal Newborn Screening for T Cell and B Cell Lymphopenia
Soma Jyonouchi, Artemio M. Jongco, Jennifer Puck, Kathleen E. Sullivan
Resolution of Primary Immune Defect in 22q11.2 Deletion Syndrome
Yiwa Suksawat, Achara Sathienkijkanchai, Jittima Veskitkul, Orathai Jirapongsananuruk, Nualanong Visitsunthorn, Pakit Vichyanond, Punchama Pacharn
Diagnostic Delay of Primary Immunodeficiencies at a Tertiary Care Hospital in Peru- Brief Report
Liz E. Veramendi-Espinoza, Jessica H. Zafra-Tanaka, Gabriela A. Pérez-Casquino, Wilmer O. Córdova-Calderón
Anti-Pneumococcal Vaccine-Induced Cellular Immune Responses in Post-Traumatic Splenectomized Individuals
Djursun Karasartova, Umut Gazi, Ozgur Tosun, Ayse S. Gureser, Ibrahim T. Sahiner, Mete Dolapci, Aysegul T. Ozkan