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Journal of Clinical Immunology

Ausgabe 8/2018

Inhalt (12 Artikel)

Editorial

William T. Shearer MD, PhD in Memoriam

Thomas A. Fleisher, Jordan S. Orange

Letter to Editor

Warts and DADA2: a Mere Coincidence?

Katrijn Arts, Jenna R. E. Bergerson, Amanda K. Ombrello, Morgan Similuk, Andrew J. Oler, Anahita Agharahimi, Emily M. Mace, Mike Hershfield, Carine Wouters, Lien De Somer, Marie-Anne Morren, Rebeca Perez-de Diego, Leen Moens, Alexandra F. Freeman, Isabelle Meyts

Letter to Editor

JAK 1/2 Blockade in MDA5 Gain-of-Function

Kirsty E. McLellan, Neil Martin, Joyce E. Davidson, Nuno Cordeiro, Bridget D. Oates, Bénédicte Neven, Gillian I. Rice, Yanick J. Crow

Letter to Editor

Three Types of Immunodeficiency, Centromeric Instability, and Facial Anomalies (ICF) Syndrome Identified by Whole-Exome Sequencing in Saudi Hypogammaglobulinemia Patients: Clinical, Molecular, and Cytogenetic Features

Hamza A. Alghamdi, Suha A. Tashkandi, Eman M. Alidrissi, Rawan D. Aledielah, Khelad A. AlSaidi, Enas S. Alharbi, Murad K. Habazi, Mofareh S. Alzahrani

Original Article

Report of a Chinese Cohort with Activated Phosphoinositide 3-Kinase δ Syndrome

Ying Wang, Wenjie Wang, Luyao Liu, Jia Hou, Wenjing Ying, Xiaoying Hui, Qinhua Zhou, Danru Liu, Haili Yao, Jinqiao Sun, Xiaochuan Wang

Open Access Original Article

Long-Term Efficacy and Safety of Hizentra® in Patients with Primary Immunodeficiency in Japan, Europe, and the United States: a Review of 7 Phase 3 Trials

Stephen Jolles, Mikhail A. Rojavin, John-Philip Lawo, Robert Nelson Jr, Richard L. Wasserman, Michael Borte, Michael A. Tortorici, Kohsuke Imai, Hirokazu Kanegane

Open Access Original Article

Home-Based Treatment with Immunoglobulins: an Evaluation from the Perspective of Patients and Healthcare Professionals

Chantal A. Zuizewind, Paul van Kessel, Christine M. Kramer, Mary M. Muijs, Janneke C. Zwiers, Mattanja Triemstra

Open Access Original Article

Treatment Satisfaction with Subcutaneous Immunoglobulin Replacement Therapy in Patients with Primary Immunodeficiency: a Pooled Analysis of Six Hizentra® Studies

Rajiv Mallick, Stephen Jolles, Hirokazu Kanegane, Dominique Agbor-Tarh, Mikhail Rojavin

Original Article

Approach to Molecular Diagnosis of Chronic Granulomatous Disease (CGD): an Experience from a Large Cohort of 90 Indian Patients

Manasi Kulkarni, Gouri Hule, Martin de Boer, Karin van Leeuwen, Priyanka Kambli, Jahnavi Aluri, Maya Gupta, Aparna Dalvi, Snehal Mhatre, Prasad Taur, Mukesh Desai, Manisha Madkaikar

Original Article

Transplantation of Hematopoietic Stem Cells for Primary Immunodeficiencies in Brazil: Challenges in Treating Rare Diseases in Developing Countries

Juliana Folloni Fernandes, Samantha Nichele, Liane E. Daudt, Rita B. Tavares, Adriana Seber, Fábio R. Kerbauy, Adriana Koliski, Gisele Loth, Ana K. Vieira, Luiz G. Darrigo-Junior, Vanderson Rocha, Alessandra A. Gomes, Vergílio Colturato, Luiz F. Mantovani, Andreza F. Ribeiro, Lisandro L. Ribeiro, Cilmara Kuwahara, Ana L. M. Rodrigues, Victor G. Zecchin, Beatriz T. Costa-Carvalho, Magda Carneiro-Sampaio, Antonio Condino-Neto, Anders Fasth, Andrew Gennery, Ricardo Pasquini, Nelson Hamerschlak, Carmem Bonfim

Original Research

Clinical and Immunological Characterization of ICF Syndrome in Japan

Chikako Kamae, Kohsuke Imai, Tamaki Kato, Tsubasa Okano, Kenichi Honma, Noriko Nakagawa, Tzu-Wen Yeh, Emiko Noguchi, Akira Ohara, Tomonari Shigemura, Hiroshi Takahashi, Shunichi Takakura, Masatoshi Hayashi, Aoi Honma, Seiichi Watanabe, Tomoko Shigemori, Osamu Ohara, Hiroyuki Sasaki, Takeo Kubota, Tomohiro Morio, Hirokazu Kanegane, Shigeaki Nonoyama

Correction

Correction to: Chronic Aichi Virus Infection in a Patient with X-Linked Agammaglobulinemia

Giorgia Bucciol, Leen Moens, Kathryn Payne, Elke Wollants, Djalila Mekahli, Elena Levtchenko, François Vermeulen, Thomas Tousseyn, Paul Gray, Cindy S. Ma, Stuart G. Tangye, Marc Van Ranst, Julianne R. Brown, Judy Breuer, Isabelle Meyts

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