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Erschienen in: Der Radiologe 12/2016

23.11.2016 | Computertomografie | Leitthema

Erkrankungen des Bindegewebes bei IgG4-assoziierten Autoimmunerkrankungen

verfasst von: Univ.-Prof. Dr. G. A. Krombach

Erschienen in: Die Radiologie | Ausgabe 12/2016

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Zusammenfassung

IgG4-assoziierte Erkrankungen des Bindegewebes beruhen auf einer allergenvermittelten Autoimmunreaktion und können das Retroperitoneum, das Mesenterium, das Mediastinum sowie seltener andere Lokalisationen (Hals, Orbita und periartikuläres Bindgewebe) betreffen. Die inflammatorische Fibrosierung mit zunächst lymphozyten- und plasmazellreichem Infiltrat und zellarmer storiformer Fibrose im späteren Stadium kann durch die Stenosierung oder den Verschluss von Gefäßen, Ureteren oder Darmschlingen schwere Komplikationen auslösen. Mithilfe von CT und MRT können die Differenzialdiagnose eingegrenzt, die Ausprägung dargestellt und Komplikationen aufgedeckt werden.
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Metadaten
Titel
Erkrankungen des Bindegewebes bei IgG4-assoziierten Autoimmunerkrankungen
verfasst von
Univ.-Prof. Dr. G. A. Krombach
Publikationsdatum
23.11.2016
Verlag
Springer Medizin
Erschienen in
Die Radiologie / Ausgabe 12/2016
Print ISSN: 2731-7048
Elektronische ISSN: 2731-7056
DOI
https://doi.org/10.1007/s00117-016-0183-x

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