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Pediatric Cardiology

Erschienen in:

01.07.2010 | Original Article

Therapeutic Strategies in Children with an Isolated Unilaterally Absent Proximal Pulmonary Artery

verfasst von: Euloge K. Krammoh, Jean-Luc Bigras, Milan Prsa, Chantal Lapierre, Joaquim Miró, Nagib S. Dahdah

Erschienen in: Pediatric Cardiology | Ausgabe 5/2010

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Abstract

Therapeutic strategies for isolated unilateral absence of a proximal pulmonary artery remain unclear. The natural history of the disease, or thrombosis of primary surgical anastomosis, leads to exclusion of the affected lung with increased risk of intrapulmonary bleeding, impaired quality of life, and shortened life expectancy. We herein describe our two-stage approach in a small series of patients starting with interventional catheterization followed by surgical anastomosis. Other medical interventions, such as anticoagulation and pulmonary vasodilatation, are key factors to successfully restore pulmonary circulation in this rare defect.

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Titel: Therapeutic Strategies in Children with an Isolated Unilaterally Absent Proximal Pulmonary Artery
verfasst von: Euloge K. Krammoh
Jean-Luc Bigras
Milan Prsa
Chantal Lapierre
Joaquim Miró
Nagib S. Dahdah
Publikationsdatum: 01.07.2010
Verlag: Springer-Verlag
Erschienen in: Pediatric Cardiology / Ausgabe 5/2010
Print ISSN: 0172-0643
Elektronische ISSN: 1432-1971
DOI: https://doi.org/10.1007/s00246-010-9689-6

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Therapeutic Strategies in Children with an Isolated Unilaterally Absent Proximal Pulmonary Artery

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