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02.02.2017 | Novel Aspects in Lupus, 2017

Thrombotic thrombocytopenic purpura in a new onset lupus patient?

verfasst von: Nery Sablón González, Noel Lorenzo, Yanet Parodis, Maria Belen Alonso Ortiz, Melek Kechida, Jose Carlos Rodriguez Perez

Erschienen in: Immunologic Research | Ausgabe 2/2017

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Abstract

We are presenting a case of TTP with undetectable levels of ADAMTS 13 in a 39-year-old woman. Diagnosis of systemic lupus was evoked in the setting of thrombotic microangiopathy. The patient presented normal renal function but important neurological impairment. Treatment with daily plasmapheresis as well as Rituximab, cyclophosphamide as steroids was required to achieve clinical improvement.

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Titel: Thrombotic thrombocytopenic purpura in a new onset lupus patient?
verfasst von: Nery Sablón González
Noel Lorenzo
Yanet Parodis
Maria Belen Alonso Ortiz
Melek Kechida
Jose Carlos Rodriguez Perez
Publikationsdatum: 02.02.2017
Verlag: Springer US
Erschienen in: Immunologic Research / Ausgabe 2/2017
Print ISSN: 0257-277X
Elektronische ISSN: 1559-0755
DOI: https://doi.org/10.1007/s12026-017-8898-y

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