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Multiple Chondromas

chondromatosis, Ollier’s disease, Maffucci’s syndrome Definition

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Bone and Soft Tissue Tumors
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Abstract

Multiple chondromas, unlike multiple exostoses, are not hereditary, are very variable in number and extent, and tend to prevail in one side of the body. When the chondromas are more extensively distributed, the term of O11ier’s disease is also employed. Multiple chondromas associated with soft tissues hemangiomas are known as Maffucci’s syndrome. Extensive multiple chondromas cause shortening and deformity of the affected bones, and undergo a frequent transformation into a chondrosarcoma.

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© 1999 Springer-Verlag Wien

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Campanacci, M. (1999). Multiple Chondromas. In: Bone and Soft Tissue Tumors. Springer, Vienna. https://doi.org/10.1007/978-3-7091-3846-5_14

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  • DOI: https://doi.org/10.1007/978-3-7091-3846-5_14

  • Publisher Name: Springer, Vienna

  • Print ISBN: 978-3-7091-3848-9

  • Online ISBN: 978-3-7091-3846-5

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