Abstract
Although in literature almost 150 patients with Lance-Adams Syndrome (LAS) have been reported, neuroradiological evaluations were often performed in late stages and there is no serial study evaluating LAS from early stages. We herein report a serial neuroimaging study demonstrating early and transient involvement of cerebellum and thalami in a LAS patient. We may hypothesize that a transient cerebral hypoxia provoked a permanent synaptic rearrangements of the neuronal networks involved in the pathogenesis of post-hypoxic myoclonus in our patient.
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Ferlazzo, E., Gasparini, S., Cianci, V. et al. Serial MRI findings in brain anoxia leading to Lance–Adams syndrome: a case report. Neurol Sci 34, 2047–2050 (2013). https://doi.org/10.1007/s10072-013-1356-2
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DOI: https://doi.org/10.1007/s10072-013-1356-2