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Multiple endocrine neoplasia type I Surgical therapy

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Endocrine Neoplasms

Part of the book series: Cancer Treatment and Research ((CTAR,volume 89))

Abstract

The therapy of MEN-I is multifaceted in that surgical treatment in the individual patient is dependent on the phenotypic expression at the time of diagnosis. In many patients, the first clinical expression of the syndrome is hyperparathyroidism (HPT). In others, it may be a combination of manifestations, including a functional endocrine pancreatic syndrome and HPT, or a combination of HPT and a pituitary tumor such as a prolactinoma. Occasionally, an MEN-I patient may present with clinical manifestations in all three organs simultaneously. This discussion will be limited to the surgical management of the parathyroid and pancreatic components of the syndrome.

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Authors
  1. Norman W. Thompson
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Editors and Affiliations

  1. Laboratory of Endocrine Oncology Massachusetts General Hospital, Harvard Medical School, Jackson 1021, Boston, MA, 02114, USA

    Andrew Arnold M.D. (Chief, Associate Professor of Medicine) (Chief, Associate Professor of Medicine)

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© 1997 Springer Science+Business Media New York

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Thompson, N.W. (1997). Multiple endocrine neoplasia type I Surgical therapy. In: Arnold, A. (eds) Endocrine Neoplasms. Cancer Treatment and Research, vol 89. Springer, Boston, MA. https://doi.org/10.1007/978-1-4615-6355-6_19

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  • DOI: https://doi.org/10.1007/978-1-4615-6355-6_19

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4613-7919-5

  • Online ISBN: 978-1-4615-6355-6

  • eBook Packages: Springer Book Archive

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