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Zusammenfassung

Beim Menschen wie bei allen Säugern, besteht ein Geschlechtsdismorphismus, d. h. es existieren zwei in Morphologie, reproduktiven Fähigkeiten und Verhalten unterschiedliche Erscheinungformen, die nur in einem heterosexuellen Zusammenwirken in der Lage sind, Nachkommen zu erzuegen. Es sollen hier nicht die erheblichen biologischen Vorteile einer solchen zunächst unökonomisch erscheinenden Form der Fortpflanzung diskutiert werden. Vielmehr soll in knapper Form der gegenwärtige Kenntnisstand über die komplexen genetischen Mechanismen erläutert werden, die zur morphologischen und funktionellen Aufrechterhaltung dieses Geschlechtsdimorphismus erforderlich sind und deren Defekte zu Störungen der genetischen Geschlechtsdeterminierung und -deferenzierung unterschiedlichen Grades bis zur Geschlechtsumkehrung, aber auch zu Störungen der seelischen Geschlechtsidentität führen können.

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© 2000 Springer-Verlag Berlin Heidelberg

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Zang, K. (2000). Störungen der Geschlechtsentwicklung. In: Wullich, B., Zang, K.D. (eds) Genetik von Krankheiten des Urogenitalsystems. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-59589-9_12

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  • DOI: https://doi.org/10.1007/978-3-642-59589-9_12

  • Publisher Name: Springer, Berlin, Heidelberg

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