Abstract
Cochlear nerve (CN) hypoplasia presents a dilemma to the implanting teams in choosing the most appropriate habilitation method. In patients with CN hypoplasia (CN deficiency), cochlear nerve has a smaller diameter than normal and usually the results of cochlear implantation (CI) are not as good as in children with normal cochlea and CN. For better outcomes, they may need a contralateral auditory brainstem implantation (ABI) during follow-up. Therefore, it is important to diagnose this condition preoperatively and counsel the family accordingly. In this chapter cochlear nerve deficiency is defined and a classification of cochlear nerve abnormalities is presented. Indications for CI and ABI are provided. Certain cases that need CI and contralateral ABI (simultaneously or consecutively) are highlighted. Finally indications for bilateral ABI are provided.
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Sennaroglu, L., Sennaroglu, G., Yücel, E. (2022). Cochlear Nerve Deficiency and Current Management of Inner Ear Malformations. In: Sennaroglu, L. (eds) Inner Ear Malformations. Springer, Cham. https://doi.org/10.1007/978-3-030-83674-0_32
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DOI: https://doi.org/10.1007/978-3-030-83674-0_32
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