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Fibrous Dysplasia, Osteofibrous Dysplasia, and Adamantinoma

  • Chapter
Imaging of Bone Tumors and Tumor-Like Lesions

Part of the book series: Medical Radiology ((Med Radiol Diagn Imaging))

Key Points

• Monostotic fibrous dysplasia is more common than polyostotic fibrous dysplasia.

• Fibrous dysplasia can be encountered in any decade of life.

• Endocrine dysfunction and soft tissue myxoma are associated with fibrous dysplasia.

• A fibrous dysplasia-like lesion with cortical destruction suggests low-grade central osteosarcoma or malignant transformation.

• Osteofibrous dysplasia usually occurs in the first two decades of life.

• Osteofibrous dysplasia almost exclusively affects the tibia and fibula.

• Adamantinoma is a rare low-grade neoplasm that most commonly occurs in the second and third decades of life.

• Adamantinoma has a strong predilection for the tibia.

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Author information

Authors and Affiliations

  1. Diagnostic Radiology/Hb6, The Cleveland Clinic Foundation, 9500 Euclid Ave., 44195, Cleveland, OH, USA

    Sriram Mannava

  2. Section of Musculoskeletal Radiology, Imaging Institute, Diagnostic Radiology/A21, School of Medicine of Case Western Reserve University, Cleveland Clinic Foundation, 9500 Euclid Ave., 44195, Cleveland, OH, USA

    Murali Sundaram

Authors
  1. Sriram Mannava
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  2. Murali Sundaram
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Editor information

Editors and Affiliations

  1. MRI Department, Royal Orthopaedic Hospital, NHS Foundation Trust, Bristol Road South, Northfield, B31 2AP, Birmingham, UK

    A. Mark Davies

  2. Section of Musculoskeletal Radiology, Imaging Institute, Diagnostic Radiology/A21, School of Medicine of Case Western Reserve University, Cleveland Clinic Foundation, 9500 Euclid Ave., 44195, Cleveland, OH, USA

    Murali Sundaram

  3. Imaging Department, Royal Orthopaedic Hospital, NHS Foundation Trust, Bristol Road South, Northfield, B31 2AP, Birmingham, UK

    Steven L. J. James

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© 2009 Springer-Verlag Berlin Heidelberg

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Mannava, S., Sundaram, M. (2009). Fibrous Dysplasia, Osteofibrous Dysplasia, and Adamantinoma. In: Davies, A., Sundaram, M., James, S. (eds) Imaging of Bone Tumors and Tumor-Like Lesions. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-77984-1_23

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  • DOI: https://doi.org/10.1007/978-3-540-77984-1_23

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-77982-7

  • Online ISBN: 978-3-540-77984-1

  • eBook Packages: MedicineMedicine (R0)

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