Abstract
Erdheim-Chester disease is a distinctive pathological radiographic entity, most commonly characterised by a typical skeletal involvement resulting from histiocytic infiltration of the bone marrow. Although lung involvement is often absent, we report a case of diffuse infiltrative lung disease characterised by a wide-spread reticular pattern on high-resolution CT scans associated with cystic airspaces and mild honeycombing observed throughout both lungs. Interstitial infiltration with lipid-laden histiocytes was histologically confirmed by means of transbronchial biopsy.
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Correspondence to: M. Remy-Jardin
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Remy-Jardin, M., Remy, J., Gosselin, B. et al. Pulmonary involvement in Erdheim-Chester disease: high-resolution CT findings. Eur. Radiol. 3, 389–392 (1993). https://doi.org/10.1007/BF00167478
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DOI: https://doi.org/10.1007/BF00167478