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Myelokathexis: Chronic neutropenia with hyperplastic bone marrow and hypersegmented neutrophils in two siblings

Myelokathexis: Chronische Neutropenie mit hyperplastischem Knochenmark und hypersegmentierten Neutrophilen bei einem Geschwisterpaar

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Zusammenfassung

Der Autor beschreibt die klinischen und pathologischen Besonderheiten einer chronischen Neutropenie bei einem Geschwisterpaar. Die Krankheit wurde wahrscheinlich autosomal rezessiv vererbt. Klinischer Verlauf und Laboratoriumsbefunde entsprachen den seltenen bisher beschriebenen Fällen von „Myelokathexis“.

Summary

The author describes the clinical and pathological characteristics of a chronic neutropenia in two siblings. The disease was probably inherited as an autosomal recessive trait. The clinical course and the results of the laboratory investigations corresponded to the rare cases of „myelokathexis“ reported so far.

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Authors and Affiliations

  1. Department of Haematology, Clinical Center, Zaloska 7, 61000, Ljubljana, Yugoslavia

    J. Bohinjec

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  1. J. Bohinjec
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Bohinjec, J. Myelokathexis: Chronic neutropenia with hyperplastic bone marrow and hypersegmented neutrophils in two siblings. Blut 42, 191–196 (1981). https://doi.org/10.1007/BF01026389

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  • DOI: https://doi.org/10.1007/BF01026389

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