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Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome

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Abstract

Type IV Ehlers-Danlos syndrome (EDS) is characterized by large vessel bleeding, visceral rupture and early death. Pulmonary complications are uncommon. We report an 18-year-old patient with EDS type IV who developed recurrent large, thick-walled lung cavitary lesions, probably a manifestation of focal lung rupture. Such hemorrhagic cavities are probably the basis of the bullous disase and recurrent pneumothoraces occasionally observed in type IV EDS.

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  1. Mallinckrodt Institute of Radiology, Washington University School of Medicine, St. Louis Children's Hospital Department of Radiology, 510 South Kingshighway Boulevard, 63110, St. Louis, MO, USA

    T. E. Herman & W. H. McAlister

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  1. T. E. Herman
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  2. W. H. McAlister
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Herman, T.E., McAlister, W.H. Cavitary pulmonary lesions in type IV Ehlers-Danlos syndrome. Pediatr Radiol 24, 263–265 (1994). https://doi.org/10.1007/BF02015451

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  • DOI: https://doi.org/10.1007/BF02015451

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