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Pulmonary Gaucher's disease: High-resolution computed tomographic features

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Abstract

CT findings in pulmonary Gaucher's disease have not been previously reported. Chest radiograph of a patient with pulmonary involvement in type I Gaucher's disease proven by biopsy showed linear and reticulo-nodular opacities. High-resolution CT demonstrated thickening of the interlobular septa and between four and six small nodules within secondary lobules, probably each corresponding to an acinus.

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Authors and Affiliations

  1. Department of Radiology, University of Istanbul, Istanbul School of Medicine, Istanbul, Turkey

    A. Tunaci & E. Gökmen

  2. Department of Radiology, Columbia-Presbyterian Medical Center, 177 Fort Washington Avenue, 10032-378, New York, NY, USA

    Y. M. Berkmen

Authors
  1. A. Tunaci
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  2. Y. M. Berkmen
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  3. E. Gökmen
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Tunaci, A., Berkmen, Y.M. & Gökmen, E. Pulmonary Gaucher's disease: High-resolution computed tomographic features. Pediatr Radiol 25, 237–238 (1995). https://doi.org/10.1007/BF02021548

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  • DOI: https://doi.org/10.1007/BF02021548

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