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Erschienen in: Head and Neck Pathology 1/2020

04.04.2019 | Case Report

Low-Grade Fibromyxoid Sarcoma of the External Auditory Canal: A Rare Pathology and Unusual Location

verfasst von: Kalpana Kumari, Ramya Thota, Heera Lal Chaudhary, Mehar C. Sharma, Alok Thakar, Geetika Singh

Erschienen in: Head and Neck Pathology | Ausgabe 1/2020

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Abstract

Low-grade fibromyxoid sarcoma (LGFMS) is an enigmatic soft tissue tumor. It frequently presents as a deeply seated mass in the proximal extremities and trunk. Superficial LGFMSs of the head and neck are exceedingly rare. Hyalinizing spindle cell tumor with giant rosettes (HSTGR) is an entity considered to be on the histologic spectrum of LGFMS. We present a case of a 44-year-old female who presented with a superficial, polypoid mass of the external auditory meatus. Microscopic examination revealed the classic histologic features of HSTGR. To our knowledge, this case is the first described at this extremely unusual location. Identification and reporting of such unusual cases is important to understand and compare the behavior of superficial LGFMS to that of the more common deeply seated tumors.
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Metadaten
Titel
Low-Grade Fibromyxoid Sarcoma of the External Auditory Canal: A Rare Pathology and Unusual Location
verfasst von
Kalpana Kumari
Ramya Thota
Heera Lal Chaudhary
Mehar C. Sharma
Alok Thakar
Geetika Singh
Publikationsdatum
04.04.2019
Verlag
Springer US
Erschienen in
Head and Neck Pathology / Ausgabe 1/2020
Elektronische ISSN: 1936-0568
DOI
https://doi.org/10.1007/s12105-019-01030-4

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