Erschienen in:
14.03.2019 | Case Report
Complete repair with unifocalization of the only unilateral lung
verfasst von:
Motonori Ishidou, Keisuke Ota, Kazuyoshi Kanno, Masaya Murata, Keiichi Hirose, Hisao Nagato, Kisaburo Sakamoto, Akio Ikai
Erschienen in:
General Thoracic and Cardiovascular Surgery
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Ausgabe 5/2020
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Abstract
A boy with 22q11.2 deletion was diagnosed with pulmonary atresia with ventricular septal defect (PAVSD) and major aortopulmonary collateral arteries (MAPCAs). At 8 months, unifocalization of left MAPCAs and BT shunt was performed at another hospital. However, they occluded directly after surgery. An angiography revealed 2 MAPCAs supplying all segments of the right lung. Qp:Qs was 2.24. At 1 year 6 months, we performed VSD closure with unifocalization of the only right lung vascularity, using intraoperative PA flow study. We report a successful case of complete repair with unilateral lung in PAVSD and MAPCAs.