Figure
A) Frontal view of patient’s face shows significant tongue and multiple lower lip AVMs, as well as bilateral neck enlargement (right greater than left) secondary to extensive AVMs in the soft tissue. B) Axial T1 post contrast MRI head. There is an enhancing extensive, multi-lobulated malformation involving the bilateral softs tissues of the neck and extension into the oronasopharynx and larynx. There is resulting oropharyngeal and laryngeal stenosis with the narrowest point measuring 10 mm × 3 mm (blue arrow). The right neck malformation extends from the peri-maxillary soft tissues down to the supraclavicular region. The malformation involves the right buccal space, lateral wall of right orbit, right masticator space, right parotid gland, right submandibular space and subcutaneous soft tissue along the sternocleidomastoid muscle. C) Sagittal T1 post contrast MRI of the head and neck. The malformation involves the lower lip, the tongue muscle, soft palate with narrowing of the oropharynx. The malformation involves bilateral pharyngeal tonsils, bilateral oropharyngeal submucosa, right carotid space, bilateral lingual spaces, right retropharyngeal submucosa. There is stenosis noted at the larynx secondary to asymmetry of malformation, greater on the right. The prevertebral space is involved bilaterally. There is less extensive malformation in the left neck. The malformation involves the left lower lip, left submandibular space around the mandibular angle, left mylohyoid muscle. There are multiple enhancing lesions in the sternal notch. Multifocal stenosis of airway (indicated by three red arrows). Narrowest point of oropharyngeal stenosis measuring 10 mm × 3 mm (indicated by top blue arrow)