A 79-year-old man with hereditary hemorrhagic telangiectasia (HHT, or Osler–Weber–Rendu syndrome) complicated by portal hypertension, hypoxemia from pulmonary shunting, congestive heart failure, and gastrointestinal bleeding was admitted for recurrent epistaxis. Examination revealed extensive telangiectasias on his back (Fig. 1) and classic blanching with pressure applied by a hand (Fig. 2).
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