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Erschienen in: Pediatric Cardiology 1/2008

01.01.2008

Chronic Granulomatous Disease Associated with Atypical Kawasaki Disease

verfasst von: M. A. Yamazaki-Nakashimada, N. Ramírez-Vargas, J. De Rubens-Figueroa

Erschienen in: Pediatric Cardiology | Ausgabe 1/2008

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Abstract

Chronic granulomatous disease (CGD) is an infrequent inherited disorder characterized by recurrent infections and abnormal granuloma formation. Patients with CGD have an exuberant inflammatory response and an increased risk of developing autoimmunity. We present the case of a 1-year-old boy with CGD who developed several of the characteristic clinical features of Kawasaki Disease. His illness responded to intravenous immunoglobulin, aspirin, and corticosteroids.
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Metadaten
Titel
Chronic Granulomatous Disease Associated with Atypical Kawasaki Disease
verfasst von
M. A. Yamazaki-Nakashimada
N. Ramírez-Vargas
J. De Rubens-Figueroa
Publikationsdatum
01.01.2008
Verlag
Springer-Verlag
Erschienen in
Pediatric Cardiology / Ausgabe 1/2008
Print ISSN: 0172-0643
Elektronische ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-007-9011-4

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