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01.01.2010 | Case Report

Post-inflammatory retinal dystrophy in CINCA syndrome

verfasst von: Donato Rigante, Achille Stabile, Angelo Minnella, Laura Avallone, Lucia Ziccardi, Giulia Bersani, Giovanna Stifano, Adele Compagnone, Benedetto Falsini

Erschienen in: Rheumatology International | Ausgabe 3/2010

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Abstract

Right chorioretinitis and bilateral pseudopapilledema were firstly appreciated in a 9-month-old child with neonatal findings of aseptic chronic meningitis, framed in the context of CINCA syndrome at 1 year. Therapeutical response to various combinations of drugs was inconsistent until 7 years, when anakinra was started with immediate clinical and laboratory improvement. A state of severe retinal dystrophy of post-inflammatory origin became evident on funduscopy, optical coherence tomography and visual electrophysiology tests at the age of 10 years, which remained stationary after 1 year of anakinra treatment.

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Titel: Post-inflammatory retinal dystrophy in CINCA syndrome
verfasst von: Donato Rigante
Achille Stabile
Angelo Minnella
Laura Avallone
Lucia Ziccardi
Giulia Bersani
Giovanna Stifano
Adele Compagnone
Benedetto Falsini
Publikationsdatum: 01.01.2010
Verlag: Springer-Verlag
Erschienen in: Rheumatology International / Ausgabe 3/2010
Print ISSN: 0172-8172
Elektronische ISSN: 1437-160X
DOI: https://doi.org/10.1007/s00296-009-0939-y

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