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Erschienen in: European Spine Journal 11/2019

22.12.2016 | Grand Rounds

The natural history of thoracolumbar kyphosis in achondroplasia

verfasst von: Malik Ahmed, Mahmoud El-Makhy, Michael Grevitt

Erschienen in: European Spine Journal | Ausgabe 11/2019

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Abstract

https://static-content.springer.com/image/art%3A10.1007%2Fs00586-016-4861-1/MediaObjects/586_2016_4861_Figa_HTML.jpg There are little published data on the natural history and evolution of thoracolumbar kyphotic deformity in achondroplasia. Furthermore, there are few published reports indicating the probability of symptoms and at what kyphotic angle progressive deformity might occur. The lack of knowledge of the fundamental natural history does not allow firm guidelines for the management of this problem. In this respect the role of bracing remains uncertain both in terms of altering the prognosis for further vertebral wedging and overall sagittal profile. This report describes three illustrative cases of thoracolumbar kyphosis (TLK) that occurred in achondroplastic infants. The long-term outcomes are presented to illustrate the diverse clinical behaviour of TLK in this patient group.
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Metadaten
Titel
The natural history of thoracolumbar kyphosis in achondroplasia
verfasst von
Malik Ahmed
Mahmoud El-Makhy
Michael Grevitt
Publikationsdatum
22.12.2016
Verlag
Springer Berlin Heidelberg
Erschienen in
European Spine Journal / Ausgabe 11/2019
Print ISSN: 0940-6719
Elektronische ISSN: 1432-0932
DOI
https://doi.org/10.1007/s00586-016-4861-1

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