The online version of this article (doi:10.1007/s00246-011-0114-6) contains supplementary material, which is available to authorized users.
Chiari’s network is a remnant of the eustachian valve located in the right atrium. Incomplete involution of the fetal sinus venosus valves results in “redundant” Chiari’s network, which may compromise cardiovascular function. This report describes a case with the novel finding of prenatal compromise due to redundant Chiari’s network and an uncommon case with significant postnatal symptoms. In both cases, the symptoms (fetal hydrops and postnatal cyanosis) resolved spontaneously. The variety of cardiovascular pathologies described in the literature is believed to be associated with persistence of a Chiari network. Knowledge about this not always harmless structure is important for perinatologists, pediatricians, and pediatric cardiologists alike. The clinical importance of this rare pathology is that prenatal counseling may anticipate a generally positive outcome and that surgical intervention generally should be avoided.
Movie Clip 1 Patient 1. Chiari network prolapsing into the right ventricle through the tricuspid valve. (MOV 958 kb)
Movie Clip 2 Patient 2. Chiari network prolapsing from the right atrium via the tricuspid valve into the right ventricle. (MOV 1194 kb)
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- Chiari’s Network as a Cause of Fetal and Neonatal Pathology
David A. van Tijn
Matthias W. Freund
Neu im Fachgebiet Kardiologie
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