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Erschienen in: Archives of Gynecology and Obstetrics 1/2010

01.01.2010 | Case Report

Leiomyomatosis peritonealis disseminata in a pregnant woman

verfasst von: Birte Summa, Christian Schem, Marion Weigel, Alexander Strauss, Walter Jonat, Nicolai Maass, Fritz Schäfer, Dirk O. Bauerschlag

Erschienen in: Archives of Gynecology and Obstetrics | Ausgabe 1/2010

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Abstract

Background

Leiomyomatosis peritonealis disseminata (LPD) is a rare disease occurring as intraabdominal benign tumors. The underlying mechanism of LPD development in premenopausal females is still unknown, but high levels of estrogen and progesterone seem to play a major role.

Case

We present a case of a 29-year-old gravida 1, 22 6/7 weeks of gestation with symptoms of an acute abdomen. Abdominal ultrasound and MRI showed intraabdominal masses of uncertain origin most likely to be an extreme example of pseudomyxoma peritonei. Explorative laparotomy was performed, and histopathological analysis revealed benign tumors classified as leiomyomatosis. A cesarean section was performed due to increasing abdominal pain and excessive elevated inflammatory serum parameters. Postpartum, a spontaneous regression of the LPD was marked.

Conclusion

LPD is a rare disease of young women. Excessive hormonal exposure seems to play a major role. Diagnosis is often difficult and a histopathological analysis is needed.
Literatur
1.
Zurück zum Zitat Bekkers RL, Willemsen WN, Schijf CP, Massuger LF, Bulten J, Merkus JM (1999) Leiomyomatosis peritonealis disseminata: does malignant transformation occur? A literature review. Gynecol Oncol 75(1):158–163CrossRefPubMed Bekkers RL, Willemsen WN, Schijf CP, Massuger LF, Bulten J, Merkus JM (1999) Leiomyomatosis peritonealis disseminata: does malignant transformation occur? A literature review. Gynecol Oncol 75(1):158–163CrossRefPubMed
2.
Zurück zum Zitat Bell DA, Weinstock MA, Scully RE (1988) Peritoneal implants of ovarian serous borderline tumors. Histologic features and prognosis. Cancer 62(10):2212–2222CrossRefPubMed Bell DA, Weinstock MA, Scully RE (1988) Peritoneal implants of ovarian serous borderline tumors. Histologic features and prognosis. Cancer 62(10):2212–2222CrossRefPubMed
3.
Zurück zum Zitat Bucher M, Pusztaszeri M, Bouzourene H (2006) Leiomyomatosis peritonealis disseminata: immunohistochemical profile and origin. Ann Pathol 26(3):207–210CrossRefPubMed Bucher M, Pusztaszeri M, Bouzourene H (2006) Leiomyomatosis peritonealis disseminata: immunohistochemical profile and origin. Ann Pathol 26(3):207–210CrossRefPubMed
4.
Zurück zum Zitat Butnor KJ, Burchette JL, Robboy SJ (1999) Progesterone receptor activity in leiomyomatosis peritonealis disseminata. Int J Gynecol Pathol 18(3):259–264PubMed Butnor KJ, Burchette JL, Robboy SJ (1999) Progesterone receptor activity in leiomyomatosis peritonealis disseminata. Int J Gynecol Pathol 18(3):259–264PubMed
5.
Zurück zum Zitat Castro-Boix S, Dopazo-Taboada C, Nadal-Guinard A, Boque-Genovard R, Zanon-Navarro V, Armengol-Carrasco M (2007) Leiomyomatosis peritonealis disseminata. Cir Esp 82(2):125–127CrossRefPubMed Castro-Boix S, Dopazo-Taboada C, Nadal-Guinard A, Boque-Genovard R, Zanon-Navarro V, Armengol-Carrasco M (2007) Leiomyomatosis peritonealis disseminata. Cir Esp 82(2):125–127CrossRefPubMed
6.
Zurück zum Zitat Clavero PA, Nogales FF, Ruiz-Avila I, Linares J, Concha A (1992) Regression of peritoneal leiomyomatosis after treatment with gonadotropin releasing hormone analogue. Int J Gynecol Cancer 2(1):52–54CrossRefPubMed Clavero PA, Nogales FF, Ruiz-Avila I, Linares J, Concha A (1992) Regression of peritoneal leiomyomatosis after treatment with gonadotropin releasing hormone analogue. Int J Gynecol Cancer 2(1):52–54CrossRefPubMed
7.
Zurück zum Zitat Daniel Y, Lessing JB, Bar-Am A, Kupferminc MJ, Jossiphov J, Peyser MR (1997) Treatment of bilateral multiple primary ovarian leiomyomas during pregnancy by way of conservative surgery: a case report. Eur J Obstet Gynecol Reprod Biol 74(2):125–126CrossRefPubMed Daniel Y, Lessing JB, Bar-Am A, Kupferminc MJ, Jossiphov J, Peyser MR (1997) Treatment of bilateral multiple primary ovarian leiomyomas during pregnancy by way of conservative surgery: a case report. Eur J Obstet Gynecol Reprod Biol 74(2):125–126CrossRefPubMed
8.
Zurück zum Zitat Due W, Pickartz H (1989) Immunohistologic detection of estrogen and progesterone receptors in disseminated peritoneal leiomyomatosis. Int J Gynecol Pathol 8(1):46–53PubMedCrossRef Due W, Pickartz H (1989) Immunohistologic detection of estrogen and progesterone receptors in disseminated peritoneal leiomyomatosis. Int J Gynecol Pathol 8(1):46–53PubMedCrossRef
9.
Zurück zum Zitat Fujii S (1981) Experimental approach to leiomyomatosis peritonealis disseminata—progesterone-induced smooth muscle-like cells in the subperitoneal nodules produced by estrogen (author’s translation). Acta Obstet Gynaecol Jpn 33(5):671–680PubMed Fujii S (1981) Experimental approach to leiomyomatosis peritonealis disseminata—progesterone-induced smooth muscle-like cells in the subperitoneal nodules produced by estrogen (author’s translation). Acta Obstet Gynaecol Jpn 33(5):671–680PubMed
10.
Zurück zum Zitat Fujii S, Nakashima N, Okamura H, Takenaka A, Kanzaki H, Okuda Y, Morimoto K, Nishimura T (1981) Progesterone-induced smooth muscle-like cells in the subperitoneal nodules produced by estrogen. Experimental approach to leiomyomatosis peritonealis disseminata. Am J Obstet Gynecol 139(2):164–172PubMed Fujii S, Nakashima N, Okamura H, Takenaka A, Kanzaki H, Okuda Y, Morimoto K, Nishimura T (1981) Progesterone-induced smooth muscle-like cells in the subperitoneal nodules produced by estrogen. Experimental approach to leiomyomatosis peritonealis disseminata. Am J Obstet Gynecol 139(2):164–172PubMed
11.
Zurück zum Zitat Haberal A, Kayikcioglu F, Caglar GS, Cavusoglu D (2007) Leiomyomatosis peritonealis disseminata presenting with intravascular extension and coexisting with endometriosis: a case report. J Reprod Med 52(5):422–424PubMed Haberal A, Kayikcioglu F, Caglar GS, Cavusoglu D (2007) Leiomyomatosis peritonealis disseminata presenting with intravascular extension and coexisting with endometriosis: a case report. J Reprod Med 52(5):422–424PubMed
12.
Zurück zum Zitat Halama N, Grauling-Halama SA, Daboul I (2005) Familial clustering of leiomyomatosis peritonealis disseminata: an unknown genetic syndrome? BMC Gastroenterol 5:33CrossRefPubMed Halama N, Grauling-Halama SA, Daboul I (2005) Familial clustering of leiomyomatosis peritonealis disseminata: an unknown genetic syndrome? BMC Gastroenterol 5:33CrossRefPubMed
13.
Zurück zum Zitat Hales HA, Peterson CM, Jones KP, Quinn JD (1992) Leiomyomatosis peritonealis disseminata treated with a gonadotropin-releasing hormone agonist. A case report. Am J Obstet Gynecol 167(2):515–516PubMed Hales HA, Peterson CM, Jones KP, Quinn JD (1992) Leiomyomatosis peritonealis disseminata treated with a gonadotropin-releasing hormone agonist. A case report. Am J Obstet Gynecol 167(2):515–516PubMed
14.
Zurück zum Zitat Hardman WJ 3rd, Majmudar B (1996) Leiomyomatosis peritonealis disseminata: clinicopathologic analysis of five cases. South Med J 89(3):291–294CrossRefPubMed Hardman WJ 3rd, Majmudar B (1996) Leiomyomatosis peritonealis disseminata: clinicopathologic analysis of five cases. South Med J 89(3):291–294CrossRefPubMed
15.
Zurück zum Zitat Herrero J, Kamali P, Kirschbaum M (1998) Leiomyomatosis peritonealis disseminata associated with endometriosis: a case report and literature review. Eur J Obstet Gynecol Reprod Biol 76(2):189–191CrossRefPubMed Herrero J, Kamali P, Kirschbaum M (1998) Leiomyomatosis peritonealis disseminata associated with endometriosis: a case report and literature review. Eur J Obstet Gynecol Reprod Biol 76(2):189–191CrossRefPubMed
16.
Zurück zum Zitat Lerwill MF, Sung R, Oliva E, Prat J, Young RH (2004) Smooth muscle tumors of the ovary: a clinicopathologic study of 54 cases emphasizing prognostic criteria, histologic variants, and differential diagnosis. Am J Surg Pathol 28(11):1436–1451CrossRefPubMed Lerwill MF, Sung R, Oliva E, Prat J, Young RH (2004) Smooth muscle tumors of the ovary: a clinicopathologic study of 54 cases emphasizing prognostic criteria, histologic variants, and differential diagnosis. Am J Surg Pathol 28(11):1436–1451CrossRefPubMed
17.
Zurück zum Zitat Lubczyk V, du Bois A, Fisseler-Eckhoff A (2005) Leiomyomatosis peritonealis disseminata and borderline lesion. Pathologe 26(4):291–295CrossRefPubMed Lubczyk V, du Bois A, Fisseler-Eckhoff A (2005) Leiomyomatosis peritonealis disseminata and borderline lesion. Pathologe 26(4):291–295CrossRefPubMed
18.
Zurück zum Zitat Roue A, Laboisse C, Winer N, Darnis E, Bouquin R, Lopes P, Philippe HJ (2007) Extra-uterine pelvic leiomyoma: diagnosis and practical management. J Gynecol Obstet Biol Reprod (Paris) 36(4):403–408 Roue A, Laboisse C, Winer N, Darnis E, Bouquin R, Lopes P, Philippe HJ (2007) Extra-uterine pelvic leiomyoma: diagnosis and practical management. J Gynecol Obstet Biol Reprod (Paris) 36(4):403–408
19.
Zurück zum Zitat Sharma P, Chaturvedi KU, Gupta R, Nigam S (2004) Leiomyomatosis peritonealis disseminata with malignant change in a post-menopausal woman. Gynecol Oncol 95(3):742–745CrossRefPubMed Sharma P, Chaturvedi KU, Gupta R, Nigam S (2004) Leiomyomatosis peritonealis disseminata with malignant change in a post-menopausal woman. Gynecol Oncol 95(3):742–745CrossRefPubMed
20.
Zurück zum Zitat Silva EG, Ross JL, Gershenson DM, Deavers MT, Malpica A (2002) Peritoneal lesions in guinea pigs treated with hormones. Int J Gynecol Pathol 21(4):412–415CrossRefPubMed Silva EG, Ross JL, Gershenson DM, Deavers MT, Malpica A (2002) Peritoneal lesions in guinea pigs treated with hormones. Int J Gynecol Pathol 21(4):412–415CrossRefPubMed
21.
Zurück zum Zitat Sobiczewski P, Bidzinski M, Radziszewski J, Panek G, Olszewski W, Tacikowska M (2004) Disseminated peritoneal leiomyomatosis—case report and literature review. Ginekol Pol 75(3):215–220PubMed Sobiczewski P, Bidzinski M, Radziszewski J, Panek G, Olszewski W, Tacikowska M (2004) Disseminated peritoneal leiomyomatosis—case report and literature review. Ginekol Pol 75(3):215–220PubMed
22.
Zurück zum Zitat Strinic T, Kuzmic-Prusac I, Eterovic D, Jakic J, Scukanec M (2000) Leiomyomatosis peritonealis disseminata in a postmenopausal woman. Arch Gynecol Obstet 264(2):97–98CrossRefPubMed Strinic T, Kuzmic-Prusac I, Eterovic D, Jakic J, Scukanec M (2000) Leiomyomatosis peritonealis disseminata in a postmenopausal woman. Arch Gynecol Obstet 264(2):97–98CrossRefPubMed
23.
Zurück zum Zitat Takeda T, Masuhara K, Kamiura S (2008) Successful management of a leiomyomatosis peritonealis disseminata with an aromatase inhibitor. Obstet Gynecol 112(2 Pt 2):491–493PubMed Takeda T, Masuhara K, Kamiura S (2008) Successful management of a leiomyomatosis peritonealis disseminata with an aromatase inhibitor. Obstet Gynecol 112(2 Pt 2):491–493PubMed
24.
Zurück zum Zitat Thian YL, Tan KH, Kwek JW, Wang J, Chern B, Yam KL (2008) Leiomyomatosis peritonealis disseminata and subcutaneous myoma—a rare complication of laparoscopic myomectomy. Abdom Imaging [Epub ahead of print] Thian YL, Tan KH, Kwek JW, Wang J, Chern B, Yam KL (2008) Leiomyomatosis peritonealis disseminata and subcutaneous myoma—a rare complication of laparoscopic myomectomy. Abdom Imaging [Epub ahead of print]
25.
Zurück zum Zitat Tripathi M, Singh PA, Tripathi A (2007) Disseminated peritoneal leiomyomatosis: a case report. Indian J Pathol Microbiol 50(2):342–344PubMed Tripathi M, Singh PA, Tripathi A (2007) Disseminated peritoneal leiomyomatosis: a case report. Indian J Pathol Microbiol 50(2):342–344PubMed
26.
Zurück zum Zitat Willson (1952) Multiple peritoneal leiomyomas associated with a granulosa-cell tumor of the ovary. Am J Obstet Gynecol 64:204–208 Willson (1952) Multiple peritoneal leiomyomas associated with a granulosa-cell tumor of the ovary. Am J Obstet Gynecol 64:204–208
27.
Zurück zum Zitat Yamaguchi T, Imamura Y, Yamamoto T, Fukuda M (2003) Leiomyomatosis peritonealis disseminata with malignant change in a man. Pathol Int 53(3):179–185CrossRefPubMed Yamaguchi T, Imamura Y, Yamamoto T, Fukuda M (2003) Leiomyomatosis peritonealis disseminata with malignant change in a man. Pathol Int 53(3):179–185CrossRefPubMed
28.
Zurück zum Zitat Zhu L, Li B (1996) Clinico-pathologic study of leiomyomatosis peritonealis disseminata. Zhonghua Bing Li Xue Za Zhi 25(5):270–272PubMed Zhu L, Li B (1996) Clinico-pathologic study of leiomyomatosis peritonealis disseminata. Zhonghua Bing Li Xue Za Zhi 25(5):270–272PubMed
Metadaten
Titel
Leiomyomatosis peritonealis disseminata in a pregnant woman
verfasst von
Birte Summa
Christian Schem
Marion Weigel
Alexander Strauss
Walter Jonat
Nicolai Maass
Fritz Schäfer
Dirk O. Bauerschlag
Publikationsdatum
01.01.2010
Verlag
Springer-Verlag
Erschienen in
Archives of Gynecology and Obstetrics / Ausgabe 1/2010
Print ISSN: 0932-0067
Elektronische ISSN: 1432-0711
DOI
https://doi.org/10.1007/s00404-009-1074-4

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