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Child's Nervous System
Erschienen in: Child's Nervous System 11/2007

01.11.2007 | Case Report

Intramedullary cavernous angioma of the spinal cord in a pediatric patient, with multiple cavernomas, familial occurrence and partial spontaneous regression: case report and review of the literature

verfasst von: Antonio Santoro, Manolo Piccirilli, Giacoma Maria Floriana Brunetto, Roberto Delfini, Giampaolo Cantore

Erschienen in: Child's Nervous System | Ausgabe 11/2007

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Abstract

Object

The authors present their experience with the 17th pediatric intramedullary cavernoma reported in English literature.

Methods

The patient firstly underwent surgery for a left frontal cavernoma when he was 2 years old. Also the child’s mother was operated for a C2–C3 intramedullary cavernoma. He grew up normally and the radiological follow-up was negative for other brainstem cavernous malformations. When he was 11 years old he complained a worsening tetraparesis. A cerebral and spinal magnetic resonance (MR) imaging revealed the presence of a C1 intramedullary cavernoma and a pontine cavernoma. He underwent surgery for the cervical lesion, which was completely removed. The postoperative course was regular with a total recovery from the neurological deficit. The boy underwent a radiological follow-up, monitoring the pontine lesion, which spontaneously regressed when he was 19 years old.

Conclusion

The rarity of the pediatric intramedullary cavernoma, the familial occurrence, and the spontaneous regression of the pontine cavernoma make this case very peculiar.
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Metadaten
Titel
Intramedullary cavernous angioma of the spinal cord in a pediatric patient, with multiple cavernomas, familial occurrence and partial spontaneous regression: case report and review of the literature
verfasst von
Antonio Santoro
Manolo Piccirilli
Giacoma Maria Floriana Brunetto
Roberto Delfini
Giampaolo Cantore
Publikationsdatum
01.11.2007
Verlag
Springer-Verlag
Erschienen in
Child's Nervous System / Ausgabe 11/2007
Print ISSN: 0256-7040
Elektronische ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-007-0395-5

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