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01.01.2008 | Case Report

Loss of vision associated with angioid streaks in β-thalassemia intermedia

verfasst von: Athanasios Aessopos, Charalampos S. Floudas, Maria Kati, Maria Tsironi, Xanthoula Giakoumi, Charalampos Livir-Rallatos, Dimitrios Farmakis

Erschienen in: International Journal of Hematology | Ausgabe 1/2008

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Abstract

An acquired diffuse elastic tissue defect that resembles inherited pseudoxanthoma elasticum (PXE) has been noticed with a significant age-related frequency in hemoglobin disorders, especially β-thalassemia and has been held responsible for a number of complications observed in these cases, some of which are quite severe. We report here two patients with β-thalassemia intermedia, who presented with severe visual acuity impairment associated with angioid streaks, the typical ocular manifestation of PXE.

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Titel: Loss of vision associated with angioid streaks in β-thalassemia intermedia
verfasst von: Athanasios Aessopos
Charalampos S. Floudas
Maria Kati
Maria Tsironi
Xanthoula Giakoumi
Charalampos Livir-Rallatos
Dimitrios Farmakis
Publikationsdatum: 01.01.2008
Verlag: Springer Japan
Erschienen in: International Journal of Hematology / Ausgabe 1/2008
Print ISSN: 0925-5710
Elektronische ISSN: 1865-3774
DOI: https://doi.org/10.1007/s12185-007-0014-y

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25.04.2024 | Nierenkarzinom | Nachrichten

Springer Medizin

Loss of vision associated with angioid streaks in β-thalassemia intermedia

Abstract

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Abstract

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