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Erschienen in: Pediatric Cardiology 4/2006

01.08.2006

Redirection of the Hepatic Venous Flow for the Treatment of Pulmonary Arteriovenous Malformations after Fontan Operation

verfasst von: Yutaka Imoto, Akira Sese, Kunitaka Joh

Erschienen in: Pediatric Cardiology | Ausgabe 4/2006

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Abstract

A 45-month-old boy who had complex cardiac anomalies with interrupted inferior vena cava and polysplenia underwent extracardiac Fontan operation. He redeveloped deep cyanosis postoperatively. Cardiac catheterization showed a preferential flow of the hepatic venous blood to the right lung and arteriovenous malformations (PAVMs) in the left lung. He underwent revision of the conduit to attain balanced hepatic venous drainage with subsequent regression of the PAVMs and disappearance of cyanosis. Our experience shows that deficiency of hepatic venous flow played a crucial role in the development of PAVMs and that redistribution of the flow retained potential to ameliorate the pathological condition.
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Metadaten
Titel
Redirection of the Hepatic Venous Flow for the Treatment of Pulmonary Arteriovenous Malformations after Fontan Operation
verfasst von
Yutaka Imoto
Akira Sese
Kunitaka Joh
Publikationsdatum
01.08.2006
Erschienen in
Pediatric Cardiology / Ausgabe 4/2006
Print ISSN: 0172-0643
Elektronische ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-006-1242-2

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