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Pediatric Surgery International

Erschienen in:

01.07.2005 | Case Report

Caudal regression syndrome—case report and review of literature

verfasst von: Santosh Kumar Singh, Rupa Dalmia Singh, Akhilesh Sharma

Erschienen in: Pediatric Surgery International | Ausgabe 7/2005

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Abstract

Caudal regression syndrome is a rare disorder of distal spinal segments affecting the development of the spinal cord, with attendant sequelae. Intelligence is preserved. The exact etiology is elusive, though maternal diabetes, genetic factors, and hypoperfusion might play roles. Recently, the role of teratogens has been studied in animal models. Treatment is difficult, multidisciplinary, and largely supportive. Lower limb deformities with sensory and motor loss and neurogenic bladder call for intensive and long-term attention.

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Titel: Caudal regression syndrome—case report and review of literature
verfasst von: Santosh Kumar Singh
Rupa Dalmia Singh
Akhilesh Sharma
Publikationsdatum: 01.07.2005
Verlag: Springer-Verlag
Erschienen in: Pediatric Surgery International / Ausgabe 7/2005
Print ISSN: 0179-0358
Elektronische ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-005-1451-4

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