Erschienen in:
06.04.2016 | Editorial
Into Action: Improving Access to Optimum Care for all Primary Immunodeficiency Patients
verfasst von:
Francisco J. Espinosa-Rosales, Antonio Condino-Neto, José L. Franco, Ricardo U. Sorensen
Erschienen in:
Journal of Clinical Immunology
|
Ausgabe 5/2016
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Excerpt
Primary Immunodeficiency (PI) is a group of over 300 inborn defects of the immune system, both in its hematopoietic as well as in its non-hematopoietic components. They can present with a broad spectrum of clinical features, either with infections (recurrent common or common lifethreatening or rare lifethreatening), autoinflammation, autoimmunity, malignancy, and or allergy. Previously classified as ‘rare diseases’ PI are no longer as rare as previously thought: today, it is estimated that PI affects more than six million people worldwide, with no gender, age or geographical boundaries. …