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Pediatric Radiology

Erschienen in:

01.09.2007 | Case Report

Congenital absence of the portal vein associated with congenital hepatic fibrosis

verfasst von: Rahsan Gocmen, Okan Akhan, Beril Talim

Erschienen in: Pediatric Radiology | Ausgabe 9/2007

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Abstract

The radiological features of a 7-year-old boy with congenital absence of the portal vein, pathologically proven congenital hepatic fibrosis, double inferior vena cava, ventricular septal defect, vertebral anomalies, crossed fused renal ectopia, and facial anomalies with pathological correlation are reported. This association between congenital absence of the portal vein and congenital hepatic fibrosis is unique.

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Titel: Congenital absence of the portal vein associated with congenital hepatic fibrosis
verfasst von: Rahsan Gocmen
Okan Akhan
Beril Talim
Publikationsdatum: 01.09.2007
Verlag: Springer-Verlag
Erschienen in: Pediatric Radiology / Ausgabe 9/2007
Print ISSN: 0301-0449
Elektronische ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-007-0533-y

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Congenital absence of the portal vein associated with congenital hepatic fibrosis

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