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Erschienen in: International Ophthalmology 3/2019

23.02.2018 | Original Paper

Management of severe persistent fetal vasculature: case series and review of the literature

verfasst von: Alon Zahavi, Dov Weinberger, Moshe Snir, Yonina Ron

Erschienen in: International Ophthalmology | Ausgabe 3/2019

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Abstract

Purpose

Persistent fetal vasculature (PFV) is a unique ocular disorder usually presenting early in life. The unregressed embryonal hyaloid vasculature poses a risk of severe ocular complications leading to decreased visual acuity. Surgery is the mainstay of therapy in complicated cases. We describe the clinical presentation and surgical treatment of PFV managed at our center from 2012 to 2015.

Methods

The study is a case series comprised eight patients who were diagnosed with complicated severe PFV. All were managed with a tailored surgical approach. The clinical characteristics, medical and surgical treatment, and follow-up findings of each case are described.

Results

There were six males and two females. Surgical intervention involved anterior or posterior vitrectomy, lens extraction, and intraocular lens implantation. Hyaloid stalk removal with release of ciliary traction was variably utilized in selected cases. Endodiathermy controlled intraocular bleeding, and intraocular scissors proved helpful in anterior PFV for disinserting the ciliary process from an abnormally thickened posterior lens capsule. Visual outcomes differed in each case, depending on multiple clinical factors.

Conclusion

Severe complex PFV presents a therapeutic challenge. A tailored surgical approach with meticulous postoperative management is essential for visual rehabilitation.
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Metadaten
Titel
Management of severe persistent fetal vasculature: case series and review of the literature
verfasst von
Alon Zahavi
Dov Weinberger
Moshe Snir
Yonina Ron
Publikationsdatum
23.02.2018
Verlag
Springer Netherlands
Erschienen in
International Ophthalmology / Ausgabe 3/2019
Print ISSN: 0165-5701
Elektronische ISSN: 1573-2630
DOI
https://doi.org/10.1007/s10792-018-0855-9

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