Erschienen in:
16.12.2014 | Case Report
Total pleural covering technique for intractable pneumothorax in patient with Ehlers–Danlos syndrome
verfasst von:
Yoshihisa Kadota, Eriko Fukui, Naoto Kitahara, Eiji Okura, Mitsunori Ohta
Erschienen in:
General Thoracic and Cardiovascular Surgery
|
Ausgabe 7/2016
Einloggen, um Zugang zu erhalten
Abstract
We report a patient with vascular-type Ehlers–Danlos syndrome (vEDS) who developed pneumothorax and was treated with a total pleural covering technique (TPC). A 24-year-old man developed repeat pneumothorax with intermittent hemo-sputum. Based on unusual radiological manifestations of lung lesions and physical findings, EDS was suspected as an underlying cause of the pneumothorax. Surgical treatment was performed using a mediastinal fat pad and TPC, and no relapse was seen up to 2 years after surgery. TPC is a less invasive surgical approach for selected patients with vEDS. Accurate underlying diagnosis of vEDS and systemic evaluation of vascular complications are necessary before planning surgery.