Erschienen in:
01.03.2011 | Case Reports
Bilateral scaphotrapezium coalition with bilateral scaphoid nonunion in a patient with Klippel–Feil syndrome: a case report
verfasst von:
Kenneth P. Unruh, Alexander Y. Shin
Erschienen in:
HAND
|
Ausgabe 1/2011
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Excerpt
The purpose of this case report is to discuss the evaluation and management of scaphoid nonunion in patients with congenital musculoskeletal syndromes. Klippel–Feil syndrome (KFS) is a rare disorder characterized by the presence of congenital synostosis of some or all cervical vertebrae [
26] caused by a failure in the normal segmentation of the cervical vertebrae during the third to the eighth week of gestation [
25]. The classic clinical triad of KFS consists of a short neck, low posterior hairline, and limited neck range of motion due to cervical synostosis [
26]. Abnormalities of the hand have been associated with KFS [
2,
4,
8,
15,
25] and are predominantly preaxial [
2,
4,
15,
25]. One instance of a postaxial anomaly in a patient with KFS has been reported [
2]. A prior identification of capitohamate coalition in a patient with Klippel–Feil syndrome was suggested to be a manifestation of a new clinical syndrome [
14]. Additional carpal coalitions have not been reported nor have scaphoid abnormalities secondary to the carpal coalitions been described that are associated with Klippel–Feil syndrome. …
