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Erschienen in:

01.12.2007

Carney’s Triad: Case Report and Review

verfasst von: R. Díaz Nieto, A. Arjona Sánchez, M. Gómez Álvarez, D. Martínez Cecilia, J. M. Sánchez Hidalgo, R. Ciria Bru, M. C. Pérez Manrique, J. Sánchez Rodríguez, S. Rufián Peña

Erschienen in: Journal of Gastrointestinal Cancer | Ausgabe 2-4/2007

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Abstract

Introduction

Carney’s triad is a rare pathogenic entity which consists of the association in young women of multiple condromatosis in the lung, gastric leiomyosarcoma, and extradrenal paraganglioma; although the presence of three at the same time is not required for its diagnosis.

Case Report

We present the case of a 27-year-old woman who was diagnosed of pulmonary multiple hamartomatosis and gastric stromal tumor.

Discussion

A review of the literature shows the most important prognosis factors and therapeutic options. Surgery for gastrointestinal stromal tumors and extradrenal paraganglioma seems to be the best treatment up to date.

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Titel: Carney’s Triad: Case Report and Review
verfasst von: R. Díaz Nieto
A. Arjona Sánchez
M. Gómez Álvarez
D. Martínez Cecilia
J. M. Sánchez Hidalgo
R. Ciria Bru
M. C. Pérez Manrique
J. Sánchez Rodríguez
S. Rufián Peña
Publikationsdatum: 01.12.2007
Verlag: Humana Press Inc
Erschienen in: Journal of Gastrointestinal Cancer / Ausgabe 2-4/2007
Print ISSN: 1941-6628
Elektronische ISSN: 1941-6636
DOI: https://doi.org/10.1007/s12029-008-9026-y

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Carney’s Triad: Case Report and Review