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26.08.2021 | Original Article

Clinical characteristics and outcomes of the right congenital diaphragmatic hernia compared to the left: a 10-year single-center experience

verfasst von: Masamune Okamoto, Hizuru Amano, Hiroo Uchida, Akinari Hinoki, Takahisa Tainaka, Chiyoe Shirota, Wataru Sumida, Kazuki Yokota, Satoshi Makita, Aitaro Takimoto, Akihiro Yasui, Yoichi Nakagawa

Erschienen in: Pediatric Surgery International | Ausgabe 12/2021

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Abstract

Purpose

The features of right-sided congenital diaphragmatic hernias (RCDHs) are quite different from those of left-sided CDHs (LCDHs). We have summarized the features of RCDHs experienced in our institution.

Methods

This retrospective study analyzed the cases of patients with CDH registered at our institution between 2011 and 2020. Defects on each side were compared based on prenatal diagnosis, medical treatment, type of surgery, and outcomes.

Results

A total of 101 patients underwent surgery at our institution during the neonatal period, and 11 had RCDHs. RCDHs and LCDHs were significantly different in terms of extracorporeal membrane oxygenation (36% vs. 6%, p = 0.002), patch repair (81% vs. 28%, p < 0.001), recurrence rate (36% vs. 11%, p = 0.022), and length of hospital stay (117 days vs. 51 days, p = 0.012). The severity of the fetal diagnosis did not reflect postnatal severity. All patients with RCDH survived to discharge, and there was no significant difference in survival rate between the right and left sides.

Conclusion

Neonates with RCDH required more intensive treatments; however, the survival rate was comparable between RCDH and LCDH. RCDH was significantly different from LCDH and an optimal treatment strategy for RCDHs should be established.

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Titel: Clinical characteristics and outcomes of the right congenital diaphragmatic hernia compared to the left: a 10-year single-center experience
verfasst von: Masamune Okamoto
Hizuru Amano
Hiroo Uchida
Akinari Hinoki
Takahisa Tainaka
Chiyoe Shirota
Wataru Sumida
Kazuki Yokota
Satoshi Makita
Aitaro Takimoto
Akihiro Yasui
Yoichi Nakagawa
Publikationsdatum: 26.08.2021
Verlag: Springer Berlin Heidelberg
Erschienen in: Pediatric Surgery International / Ausgabe 12/2021
Print ISSN: 0179-0358
Elektronische ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-021-04999-8

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Clinical characteristics and outcomes of the right congenital diaphragmatic hernia compared to the left: a 10-year single-center experience

Abstract

Purpose

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Results

Conclusion

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