Erschienen in:
16.03.2016 | Case Report
Intraspinal extradural benign fibrous histiocytoma of the lumbar spine in a pediatric patient. Case report and literature review
verfasst von:
Fabrizio Donati, Luca Proietti, Aaron Burrofato, Domenico Alessandro Santagada, Francesco Ciro Tamburrelli
Erschienen in:
Child's Nervous System
|
Ausgabe 8/2016
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Abstract
Introduction
Benign fibrous histiocytoma (BFH) is a rare skeletal tumor. Spinal localizations have been previously described in 17 cases, and this is the first report of BFH occurring at the lumbar spine in a pediatric patient.
Case report
A 13-year-old male complained lower limb motor and sensory impairment with severe claudication and urination disorders. A huge intraspinal, extradural mass at L4–L5 level, clearly evident on a preoperative MRI, caused dislocation and severe compression of the cauda equina nerve roots. After a biopsy, confirming BFH, a tumor resection and L4–S1 vertebral arthrodesis was carried out. At 1 year follow–up, no recurrence was detached on postoperative MRI, with complete neurological recovery.
Discussion and conclusion
Review of the literature is discussed. Histological examination is mandatory for a correct diagnosis and plan of treatment. None of the pediatric patients treated for BFH have ever shown local relapse.