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Journal of Clinical Immunology

Ausgabe 6/2014

Inhalt (16 Artikel)

Astute Clinician Report

Clinical Heterogeneity of Immunodysregulation, Polyendocrinopathy, Enteropathy, X-linked: Pulmonary Involvement as a Non-Classical Disease Manifestation

Safa Baris, Ilka Schulze, Ahmet Ozen, Elif Karakoc Aydiner, Emel Altuncu, Gulsun Tezcan Karasu, Nilufer Ozturk, Myriam Lorenz, Klaus Schwarz, Thomas Vraetz, Stephan Ehl, Isil B. Barlan

Astute Clinician Report

Tetratricopeptide Repeat Domain 7A (TTC7A) Mutation in a Newborn with Multiple Intestinal Atresia and Combined Immunodeficiency

Niti Sardana Agarwal, Lesley Northrop, Kwame Anyane-Yeboa, Vimla S. Aggarwal, Peter L. Nagy, Yesim Yilmaz Demirdag

Astute Clinician Report

SCIg vs IVIg: Let’s Give Patients the Choice!

K. Samaan, M. C. Levasseur, H. Decaluwe, C. St-Cyr, H. Chapdelaine, A. Des Roches, E. Haddad

Original Research

Ill-Defined Germinal Centers and Severely Reduced Plasma Cells are Histological Hallmarks of Lymphadenopathy in Patients with Common Variable Immunodeficiency

Susanne Unger, Maximilian Seidl, Annette Schmitt-Graeff, Joachim Böhm, Klaudia Schrenk, Claudia Wehr, Sigune Goldacker, Ruth Dräger, Barbara C. Gärtner, Paul Fisch, Martin Werner, Klaus Warnatz

Original Research

Autoimmunity and Inflammation in X-linked Agammaglobulinemia

Vivian P. Hernandez-Trujillo, Chris Scalchunes, Charlotte Cunningham-Rundles, Hans D. Ochs, Francisco A. Bonilla, Ken Paris, Leman Yel, Kathleen E. Sullivan

Original Research

Clinical and Molecular Features of 38 Children with Chronic Granulomatous Disease in Mainland China

Huan Xu, Wen Tian, Shu-Juan Li, Lu-Ying Zhang, Wei Liu, Yao Zhao, Zhi-Yong Zhang, Xue-Mei Tang, Mo Wang, Dao-Qi Wu, Ji-Sheng Shi, Yuan Ding, Xiao-Dong Zhao, Xi-Qiang Yang, Li-Ping Jiang

Original Research

CT Screening for Pulmonary Pathology in Common Variable Immunodeficiency Disorders and the Correlation with Clinical and Immunological Parameters

L. J. Maarschalk-Ellerbroek, P. A. de Jong, J. M. van Montfrans, J. W. J. Lammers, A. C. Bloem, A. I. M. Hoepelman, P. M. Ellerbroek

Original Research

High Level Antibody Avidity is Achieved in HIV-Seropositive Recipients of an Inactivated Split Adjuvanted (AS03A) Influenza Vaccine

Karen K. Yam, Erica Gipson, Marina Klein, Sharon Walmsley, David Haase, Scott Halperin, David Scheifele, Brian J. Ward, Curtis Cooper

Original Research

Early Systemic Sclerosis: Serum Profiling of Factors Involved in Endothelial, T-cell, and Fibroblast Interplay is Marked by Elevated Interleukin-33 Levels

Serena Vettori, Giovanna Cuomo, Michele Iudici, Virginia D’Abrosca, Veronica Giacco, Giusi Barra, Raffaele De Palma, Gabriele Valentini

Original Research

Recombinant Domain V of β2-Glycoprotein I Inhibits the Formation of Atherogenic oxLDL/β2-Glycoprotein I Complexes

Jingda Li, Yan Chi, Shuqian Liu, Le Wang, Renjun Wang, Xiaofei Han, Eiji Matsuura, Qingping Liu

Brief Communication

Major Histocompatibility Complex Class II Deficiency Complicated by Mycobacterium avium Complex in a Boy of Mixed Ethnicity

Dimana Dimitrova, Peck Y. Ong, Maurice R. G. O’Gorman, Joseph A. Church

Brief Communication

Autologous Human Cytomegalovirus-Specific Cytotoxic T Cells as Rescue Therapy for Ulcerative Enteritis in Primary Immunodeficiency

Rachele Ciccocioppo, Patrizia Comoli, Alessandra Gallia, Sabrina Basso, Fausto Baldanti, Gino Roberto Corazza

Brief Communication

Novel NFKB2 Mutation in Early-Onset CVID

Yiwen Liu, Steven Hanson, Padmalal Gurugama, Alison Jones, Barnaby Clark, Mohammad A A Ibrahim

Brief Communication

A Complement Factor B Mutation in a Large Kindred with Atypical Hemolytic Uremic Syndrome

Michinori Funato, Osamu Uemura, Katsumi Ushijima, Hidenori Ohnishi, Kenji Orii, Zenichiro Kato, Satoshi Yamakawa, Takuhito Nagai, Osamu Ohara, Hideo Kaneko, Naomi Kondo

Erratum

Erratum to: TH1/TH2 Functional Imbalance After Acute Myocardial Infarction: Coronary Arterial Inflammation or Myocardial Inflammation

Xiang Cheng, Yu-hua Liao, Hongxia Ge, Bin Li, Jinying Zhang, Jing Yuan, Min Wang, Ying Liu, Zhangqiang Guo, Jing Chen, Jin Zhang, Lanjing Zhang

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