Ausgabe 6/2014
Inhalt (16 Artikel)
Clinical Heterogeneity of Immunodysregulation, Polyendocrinopathy, Enteropathy, X-linked: Pulmonary Involvement as a Non-Classical Disease Manifestation
Safa Baris, Ilka Schulze, Ahmet Ozen, Elif Karakoc Aydiner, Emel Altuncu, Gulsun Tezcan Karasu, Nilufer Ozturk, Myriam Lorenz, Klaus Schwarz, Thomas Vraetz, Stephan Ehl, Isil B. Barlan
Tetratricopeptide Repeat Domain 7A (TTC7A) Mutation in a Newborn with Multiple Intestinal Atresia and Combined Immunodeficiency
Niti Sardana Agarwal, Lesley Northrop, Kwame Anyane-Yeboa, Vimla S. Aggarwal, Peter L. Nagy, Yesim Yilmaz Demirdag
SCIg vs IVIg: Let’s Give Patients the Choice!
K. Samaan, M. C. Levasseur, H. Decaluwe, C. St-Cyr, H. Chapdelaine, A. Des Roches, E. Haddad
Ill-Defined Germinal Centers and Severely Reduced Plasma Cells are Histological Hallmarks of Lymphadenopathy in Patients with Common Variable Immunodeficiency
Susanne Unger, Maximilian Seidl, Annette Schmitt-Graeff, Joachim Böhm, Klaudia Schrenk, Claudia Wehr, Sigune Goldacker, Ruth Dräger, Barbara C. Gärtner, Paul Fisch, Martin Werner, Klaus Warnatz
Autoimmunity and Inflammation in X-linked Agammaglobulinemia
Vivian P. Hernandez-Trujillo, Chris Scalchunes, Charlotte Cunningham-Rundles, Hans D. Ochs, Francisco A. Bonilla, Ken Paris, Leman Yel, Kathleen E. Sullivan
Clinical and Molecular Features of 38 Children with Chronic Granulomatous Disease in Mainland China
Huan Xu, Wen Tian, Shu-Juan Li, Lu-Ying Zhang, Wei Liu, Yao Zhao, Zhi-Yong Zhang, Xue-Mei Tang, Mo Wang, Dao-Qi Wu, Ji-Sheng Shi, Yuan Ding, Xiao-Dong Zhao, Xi-Qiang Yang, Li-Ping Jiang
CT Screening for Pulmonary Pathology in Common Variable Immunodeficiency Disorders and the Correlation with Clinical and Immunological Parameters
L. J. Maarschalk-Ellerbroek, P. A. de Jong, J. M. van Montfrans, J. W. J. Lammers, A. C. Bloem, A. I. M. Hoepelman, P. M. Ellerbroek
High Level Antibody Avidity is Achieved in HIV-Seropositive Recipients of an Inactivated Split Adjuvanted (AS03A) Influenza Vaccine
Karen K. Yam, Erica Gipson, Marina Klein, Sharon Walmsley, David Haase, Scott Halperin, David Scheifele, Brian J. Ward, Curtis Cooper
Early Systemic Sclerosis: Serum Profiling of Factors Involved in Endothelial, T-cell, and Fibroblast Interplay is Marked by Elevated Interleukin-33 Levels
Serena Vettori, Giovanna Cuomo, Michele Iudici, Virginia D’Abrosca, Veronica Giacco, Giusi Barra, Raffaele De Palma, Gabriele Valentini
Recombinant Domain V of β2-Glycoprotein I Inhibits the Formation of Atherogenic oxLDL/β2-Glycoprotein I Complexes
Jingda Li, Yan Chi, Shuqian Liu, Le Wang, Renjun Wang, Xiaofei Han, Eiji Matsuura, Qingping Liu
Major Histocompatibility Complex Class II Deficiency Complicated by Mycobacterium avium Complex in a Boy of Mixed Ethnicity
Dimana Dimitrova, Peck Y. Ong, Maurice R. G. O’Gorman, Joseph A. Church
Autologous Human Cytomegalovirus-Specific Cytotoxic T Cells as Rescue Therapy for Ulcerative Enteritis in Primary Immunodeficiency
Rachele Ciccocioppo, Patrizia Comoli, Alessandra Gallia, Sabrina Basso, Fausto Baldanti, Gino Roberto Corazza
Novel NFKB2 Mutation in Early-Onset CVID
Yiwen Liu, Steven Hanson, Padmalal Gurugama, Alison Jones, Barnaby Clark, Mohammad A A Ibrahim
A Complement Factor B Mutation in a Large Kindred with Atypical Hemolytic Uremic Syndrome
Michinori Funato, Osamu Uemura, Katsumi Ushijima, Hidenori Ohnishi, Kenji Orii, Zenichiro Kato, Satoshi Yamakawa, Takuhito Nagai, Osamu Ohara, Hideo Kaneko, Naomi Kondo
Erratum to: TH1/TH2 Functional Imbalance After Acute Myocardial Infarction: Coronary Arterial Inflammation or Myocardial Inflammation
Xiang Cheng, Yu-hua Liao, Hongxia Ge, Bin Li, Jinying Zhang, Jing Yuan, Min Wang, Ying Liu, Zhangqiang Guo, Jing Chen, Jin Zhang, Lanjing Zhang