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Journal of Clinical Immunology

Ausgabe 8/2023

Inhalt (59 Artikel)

“The Regimental Pediatrician”: the Finnish Child Refugees and the Temporary Children’s Hospital

  • Commentary

Rolf Kostmann

“The Regimental Pediatrician”: the Patients and the Work in the Early Years

  • Commentary

Rolf Kostmann

“The Regimental Paediatrician”: the New Children’s Hospital

  • Commentary

Rolf Kostmann

Phenotypic Variability in PRKCD: a Review of the Literature

  • CME Review

Lucy Jefferson, Athimalaipet Vaidyanathan Ramanan, Stephen Jolles, Jolanta Bernatoniene, Anne-Laure Mathieu, Alexandre Belot, Marion Ruth Roderick

Infection and Vaccine Induced Spike Antibody Responses Against SARS-CoV-2 Variants of Concern in COVID-19-Naïve Children and Adults

  • Open Access
  • Original Article

Aleha Pillay, Avani Yeola, Fiona Tea, Martina Denkova, Samuel Houston, Rebecca Burrell, Vera Merheb, Fiona X. Z. Lee, Joseph A. Lopez, Lilly Moran, Ajay Jadhav, Katrina Sterling, Catherine L. Lai, Tennille L. Vitagliano, Anupriya Aggarwal, Dan Catchpoole, Nicholas Wood, Tri Giang Phan, Ralph Nanan, Peter Hsu, Stuart G. Turville, Philip N. Britton, Fabienne Brilot

Both Humoral and Cellular Immune Responses to SARS-CoV-2 Are Essential to Prevent Infection: a Prospective Study in a Working Vaccinated Population from Southern France

  • Open Access
  • Original Article

Daisy Graça, Vesna Brglez, Jonathan Allouche, Kévin Zorzi, Céline Fernandez, Maxime Teisseyre, Marion Cremoni, Sylvia Benzaken, Christian Pradier, Barbara Seitz-Polski

Hyper-IgD Syndrome: Caused by Deficiency on Ras Prenylation and Trained Immunity?

  • Letter to Editor

Rafael Cardoso Maciel Costa Silva

Split Immunological Reconstitution in a NEMO-Deficient Male with Incontinentia Pigmenti and Immunodeficiency

  • Letter to Editor

Motoshi Sonoda, Masataka Ishimura, Reina Ogata, Hirotsugu Oda, Shouichi Ohga

Somatic Genetic Reversion of a Duplication Event in IL2RG in Siblings

  • Letter to Editor

Patricia dela Cruz, Stacey Rylaarsdam, Troy R. Torgerson, David Hagin, Eric J. Allenspach

A Case Report of Folliculin-Interacting Protein 1 Deficiency

  • Letter to Editor

Nidia Moreno-Corona, Alice Valagussa, Romane Thouenon, Alain Fischer, Sven Kracker

Soluble Interleukin-2 Receptor/White Blood Cell Ratio Reflects Granulomatous Disease Progression in Common Variable Immune Deficiency

  • Open Access
  • Letter to Editor

Astrid C. van Stigt, Virgil A. S. H. Dalm, Nicole M. A. Nagtzaam, P. Martin van Hagen, Willem A. Dik, Hanna IJspeert

Haploidentical Stem Cell Transplantation with Post-transplantation Cyclophosphamide in High-Risk Chronic Granulomatous Disease Patient with Invasive Mucormycosis

  • Letter to Editor

D. Ruttens, P. Philippet, Bénédicte Neven, Katrien Lagrou, Despina Moshous, G. Bucciol, I. Meyts

JAK Inhibition with Baricitinib for Severe CVID-Related Enteropathy: a Case Report

  • Letter to Editor

Amir Abdelmoumen, Joris van Montfrans, Femke van Wijk, Helen Leavis

Early Diagnosis of Ataxia Telangiectasia Through Newborn Screening for SCID: a Case Report Highlighting the Dilemma of Pre-emptive HSCT

  • Letter to Editor

T. J. Weitering, M. A. A. P. Willemsen, A. M. R. Taylor, C. M. R. Weemaes, M. van der Burg, Dagmar Berghuis

APECED Rash as the First Manifestation of APECED Syndrome

  • Letter to Editor

Elise M. N. Ferré, Chyi-Chia R. Lee, Heidi H. Kong, Edward W. Cowen, Michail S. Lionakis

Novel IFNGR1 Mutation in a Child with Mycobacterium avium Infection

  • Letter to Editor

Qi Luo, Runci Wang, Qiong Fu, Feng Chen, Zhen Tan

Enterobacter cloacae, a Rare Cause of Cervical Lymphadenitis in X-Linked Chronic Granulomatous Disease

  • Letter to Editor

Cooper Penner, Rahul Datta, Jefferson Ebube, Neil Romberg

Identification of a Novel Nonsense Mutation in NFKB1 Causing Common Variable Immunodeficiency with Decreased Tfh Cells

  • Letter to Editor

Rui Li, Jinjing Qian, Runci Wang, Chunmei Wu, Qiong Fu, Liangjing Lu

Novel ADA2 Variants in a Romanian Case Series of DADA2

  • Letter to Editor

Alexis Virgil Cochino, Andreea Ioan, Oana Maria Farkas, Meng Liu, Pui Y. Lee

The Immune Status of Patients with 16p11.2 Deletion Syndrome

  • Letter to Editor

Laura A. Wang, Austin Larson, Jordan K. Abbott

Disseminated Histoplasmosis in a Brazilian Patient with G6PD Deficiency Caused by Class I Variant

  • Letter to Editor

Ranieri Coelho Salgado, Lillian Nunes Gomes, Tábata Takahashi França, Sarah Maria da Silva Napoleão, Lucila Akune Barreiros, Tiago Santos de Oliveira, Edson Kiyotaka Ishizuka, Janaira Fernandes Severo Ferreira, Antonio Condino-Neto

Chronic Granulomatous Disease: a Cohort of 173 Patients—10-Years Single Center Experience from Egypt

  • Open Access
  • Original Article

Dalia Abd Elaziz, Rabab EL Hawary, Safa Meshaal, Radwa Alkady, Sohilla Lotfy, Alia Eldash, Aya Erfan, Engy Chohayeb, Mai Saad, Jeannette Boutros, Nermeen Galal, Aisha Elmarsafy

Outcome of Second Allogeneic HSCT for Patients with Inborn Errors of Immunity: Retrospective Study of 20 Years’ Experience

  • Original Article

Priti Mehta, Christo Tsilifis, Su Han Lum, Mary A. Slatter, Sophie Hambleton, Stephen Owens, Eleri Williams, Terry Flood, Andrew R. Gennery, Zohreh Nademi

An International Survey of Allogeneic Hematopoietic Cell Transplantation for X-Linked Agammaglobulinemia

  • Original Article

Akira Nishimura, Ramya Uppuluri, Revathi Raj, Venkateswaran Vellaichamy Swaminathan, Yifei Cheng, Rolla F. Abu-Arja, Bin Fu, Alexandra Laberko, Michael H. Albert, Fabian Hauck, Giorgia Bucciol, Venetia Bigley, Suzanne Elcombe, Gaurav Kharya, Cornelis Jan H Pronk, Claudia Wehr, Bénédicte Neven, Klaus Warnatz, Isabelle Meyts, Tomohiro Morio, Andrew R. Gennery, Hirokazu Kanegane

Immunologic and Genetic Contributors to CD46-Dependent Immune Dysregulation

  • Open Access
  • Original Article

Benedikt J Meyer, Natalia Kunz, Sayuri Seki, Rebecca Higgins, Adhideb Ghosh, Robin Hupfer, Adrian Baldrich, Julia R Hirsiger, Annaïse J Jauch, Anne-Valérie Burgener, Jonas Lötscher, Markus Aschwanden, Michael Dickenmann, Mihaela Stegert, Christoph T Berger, Thomas Daikeler, Ingmar Heijnen, Alexander A Navarini, Christoph Rudin, Hiroyuki Yamamoto, Claudia Kemper, Christoph Hess, Mike Recher

Correction to: Immunologic and Genetic Contributors to CD46‑Dependent Immune Dysregulation

  • Open Access
  • Correction

Benedikt J Meyer, Natalia Kunz, Sayuri Seki, Rebecca Higgins, Adhideb Ghosh, Robin Hupfer, Adrian Baldrich, Julia R Hirsiger, Annaïse J Jauch, Anne-Valerie Burgener, Jonas Lötscher, Markus Aschwanden, Michael Dickenmann, Mihaela Stegert, Christoph T Berger, Thomas Daikeler, Ingmar Heijnen, Alexander A Navarini, Christoph Rudin, Hiroyuki Yamamoto, Claudia Kemper, Christoph Hess, Mike Recher

Inborn Errors of Immunity—the Sri Lankan Experience 2010–2022

  • Original Article

Dhanushka Dasanayake, Jacinta Bustamante, Stéphanie Boisson–Dupuis, Chandima Karunatilleke, James Thambyrajah, Anne Puel, Koon Wing Chan, Rainer Doffinger, Yu-Lung Lau, Jean-Laurent Casanova, Dinakantha Kumararatne, Rajiva de Silva

Screening for Antibody Deficiencies in Adults by Serum Electrophoresis and Calculated Globin

  • Original Article

Cristina Frias Sartorelli de Toledo Piza, Carolina Sanchez Aranda, Dirceu Solé, Stephen Jolles, Antonio Condino-Neto

Correction to: Screening for Antibody Deficiencies in Adults by Serum Electrophoresis and Calculated Globulin

  • Correction

Cristina Frias Sartorelli de Toledo Piza, Carolina Sanchez Aranda, Dirceu Solé, Stephen Jolles, Antonio Condino-Neto

Atypical Localization of Eczema Discriminates DOCK8 or STAT3 Deficiencies from Atopic Dermatitis

  • Original Article

Nurhan Kasap, Altan Kara, Velat Celik, Sevgi Bilgic Eltan, Idil Akay Haci, Hulya Kose, Ayse Aygun, Emre Akkelle, Nalan Yakici, Sukru Nail Guner, Ismail Reisli, Sevgi Keles, Sukru Cekic, Sara Sebnem Kilic, Neslihan Edeer Karaca, Nesrin Gulez, Ferah Genel, Ahmet Ozen, Ayse Deniz Yucelten, Elif Karakoc-Aydiner, Klaus Schmitz-Abe, Safa Baris

A Clinical Conundrum with Diagnostic and Therapeutic Challenge: a Tale of Two Disorders in One Case

  • Original Article

Pallavi Gaikwad, Umair Ahmed Bargir, Shweta Shinde, Pranoti Kini, Rajesh Chaurasia, Usha Yadav, Amruta Dhawale, Merin George, Neha Jodhawat, Priyanka Setia, Disha Vedpathak, Aparna Dalvi, Ankita Parab, Maya Gupta, Reetika Malik Yadav, Mayuri Goriwale, Baburao Vundinti, Nagesh Bhat, B. K. Sapra, Madhumati Otiv, Ratna Sharma, Manisha Madkaikar

Common and Uncommon CT Findings in CVID-Related GL-ILD: Correlations with Clinical Parameters, Therapeutic Decisions and Potential Implications in the Differential Diagnosis

  • Open Access
  • Original Article

Riccardo Scarpa, Francesco Cinetto, Cinzia Milito, Sabrina Gianese, Valentina Soccodato, Helena Buso, Giulia Garzi, Maria Carrabba, Emanuele Messina, Valeria Panebianco, Carlo Catalano, Giovanni Morana, Vassilios Lougaris, Nicholas Landini, Maria Pia Bondioni

A Narrative Review of the Neurological Manifestations of Human Adenosine Deaminase 2 Deficiency

  • Open Access
  • Original Article

Mariia Dzhus, Lisa Ehlers, Marjon Wouters, Katrien Jansen, Rik Schrijvers, Lien De Somer, Steven Vanderschueren, Marco Baggio, Leen Moens, Benjamin Verhaaren, Rik Lories, Giorgia Bucciol, Isabelle Meyts

A Novel CDC42 Variant with Impaired Thymopoiesis, IL-7R Signaling, PAK1 Binding, and TCR Repertoire Diversity

  • Open Access
  • Original Article

Kristian Assing, Sofie E. Jørgensen, Katrine S. Sandgaard, Kerstin De Keukeleere, Marie B.-Hansen, Mikkel S. Petersen, Ulla B. Hartling, Thanis M. K.-de Vaal, Christian Nielsen, Marianne A. Jakobsen, Eleanor Watt, Stuart Adams, Qin Hao, Christina Fagerberg, Trine H. Mogensen

Clinical, Immunological, and Genetic Findings in Iranian Patients with MHC-II Deficiency: Confirmation of c.162delG RFXANK Founder Mutation in the Iranian Population

  • Original Article

Mohadese Sadat Mousavi Khorshidi, Yoann Seeleuthner, Zahra Chavoshzadeh, Maryam Behfar, Amir Ali Hamidieh, Hosein Alimadadi, Roya Sherkat, Tooba Momen, Nasrin Behniafard, Shabnam Eskandarzadeh, Mahboubeh Mansouri, Mahdiyeh Behnam, Mohadese Mahdavi, Maryam Heydarazad Zadeh, Mehdi Shokri, Fatemeh Alizadeh, Mahshid Movahedi, Mana Momenilandi, Mohammad Keramatipour, Jean-Laurent Casanova, Aurélie Cobat, Laurent Abel, Mohammad Shahrooei, Nima Parvaneh

Molecular Challenges in the Diagnosis of X-Linked Chronic Granulomatous Disease: CNVs, Intronic Variants, Skewed X-Chromosome Inactivation, and Gonosomal Mosaicism

  • Original Article

Laura Batlle-Masó, Jacques G. Rivière, Clara Franco-Jarava, Andrea Martín-Nalda, Marina Garcia-Prat, Alba Parra-Martínez, Aina Aguiló-Cucurull, Neus Castells, Mónica Martinez-Gallo, Pere Soler-Palacín, Roger Colobran

Allogeneic HSCT for Symptomatic Female X-linked Chronic Granulomatous Disease Carriers

  • Open Access
  • Original Article

Christo Tsilifis, Tuulia Torppa, Eleri J. Williams, Michael H. Albert, Fabian Hauck, Elena Soncini, Elizabeth Kang, Harry Malech, Catharina Schuetz, Horst von Bernuth, Mary A. Slatter, Andrew R. Gennery

Systematic Approach Revealed SERPING1 Splicing-Affecting Variants to be Highly Represented in the Czech National HAE Cohort

  • Open Access
  • Original Article

Hana Grombirikova, Viktor Bily, Premysl Soucek, Michal Kramarek, Roman Hakl, Lucie Ballonova, Barbora Ravcukova, Dita Ricna, Karolina Kozena, Lucie Kratochvilova, Marta Sobotkova, Radana Zachova, Pavel Kuklinek, Pavlina Kralickova, Irena Krcmova, Jana Hanzlikova, Martina Vachova, Olga Krystufkova, Eva Dankova, Milos Jesenak, Martina Novackova, Michal Svoboda, Jiri Litzman, Tomas Freiberger

Severe RAS-Associated Lymphoproliferative Disease Case with Increasing αβ Double-Negative T Cells with Atypical Features

  • Original Article

Daisuke Kurita, Norio Shiba, Takashi Ohya, Ayako Murase, Yuko Shimosato, Masahiro Yoshitomi, Seira Hattori, Koji Sasaki, Kenichi Nishimura, Shin-ichi Tsujimoto, Masanobu Takeuchi, Reo Tanoshima, Hirokazu Kanegane, Norihiko Kitagawa, Shuichi Ito

Proteomic Analysis of Pediatric Hemophagocytic Lymphohistiocytosis: a Comparative Study with Healthy Controls, Sepsis, Critical Ill, and Active Epstein-Barr virus Infection to Identify Altered Pathways and Candidate Biomarkers

  • Open Access
  • Original Article

Xun Li, Ting Luo, Haipeng Yan, Longlong Xie, Yufan Yang, Ling Gong, Zhexuan Tang, Minghui Tang, Xinping Zhang, Jiaotian Huang, Mincui Zheng, Zhenya Yao, Ping Zang, Desheng Zhu, Zhenghui Xiao, Xiulan Lu

A Novel Homozygous Mutation Causing Complete TYK2 Deficiency, with Severe Respiratory Viral Infections, EBV-Driven Lymphoma, and Jamestown Canyon Viral Encephalitis

  • Original Article

Lucie Roussel, Anne Pham-Huy, Andrea C. Yu, Sunita Venkateswaran, Anna Perez, Guillaume Bourdel, Yichun Sun, Stephanya Tellez Villavicencio, Stéphane Bernier, Yongbiao Li, Makayla Kazimerczak-Brunet, Rolan Alattar, Marc-André Déry, Adam J. Shapiro, Justin Penner, Donald C. Vinh

Clinical Validation of a Primary Antibody Deficiency Screening Algorithm for Primary Care

  • Open Access
  • Original Article

Marianne A. Messelink, Paco M. J. Welsing, Giovanna Devercelli, Jan Willem N. Marsden, Helen L. Leavis

Peripheral T Cell Populations are Differentially Affected in Familial Mediterranean Fever, Chronic Granulomatous Disease, and Gout

  • Open Access
  • Original Article

Burcu Al, Mariolina Bruno, Rutger J. Röring, Simone J. C. F. M. Moorlag, Tsz Kin Suen, Viola Klück, Ruiqi Liu, Priya A. Debisarun, Orsolya Gaal, Jaydeep Bhat, Dieter Kabelitz, Frank L. van de Veerdonk, Leo A.B. Joosten, Mihai G. Netea, Katarzyna Placek

Tuberculosis and Bacillus Calmette-Guérin Disease in Patients with Chronic Granulomatous Disease: an Experience from a Tertiary Care Center in North India

  • Original Article

Pandiarajan Vignesh, Archan Sil, Ridhima Aggarwal, Wrik Laha, Sanjib Mondal, Manpreet Dhaliwal, Saniya Sharma, Rakesh Kumar Pilania, Ankur Kumar Jindal, Deepti Suri, Sunil Sethi, Amit Rawat, Surjit Singh

Neurologic Status of Patients with Purine Nucleoside Phosphorylase Deficiency Before and After Hematopoetic Stem Cell Transplantation

  • Original Article

Betul Gemici Karaaslan, Isilay Turan, Sezin Aydemir, Zeynep Akyuncu Meric, Didem Atay, Arzu Akcay, Aysun Ayaz Sari, Michael Hershfield, Funda Cipe, Basak Adakli Aksoy, Gizem Zengin Ersoy, Ceyhun Bozkurt, Yasemin Kendir Demirkol, Gulyuz Ozturk, Cigdem Aydogmus, Ayca Kiykim, Haluk Cokugras

Functional Relevance of CTLA4 Variants: an Upgraded Approach to Assess CTLA4-Dependent Transendocytosis by Flow Cytometry

  • Open Access
  • Original Article

Jessica Rojas-Restrepo, Elena Sindram, Simon Zenke, Hanna Haberstroh, Noriko Mitsuiki, Annemarie Gabrysch, Katrin Huebscher, Sara Posadas-Cantera, Máté Krausz, Robin Kobbe, Jan C. Rohr, Bodo Grimbacher, Laura Gámez-Díaz

Correction to: Functional Relevance of CTLA4 Variants: an Upgraded Approach to Assess CTLA4‑Dependent Transendocytosis by Flow Cytometry

  • Open Access
  • Correction

Jessica Rojas‑Restrepo, Elena Sindram, Simon Zenke, Hanna Haberstroh, Noriko Mitsuiki, Annemarie Gabrysch, Katrin Huebscher, Sara Posadas‑Cantera, Máté Krausz, Robin Kobbe, Jan C. Rohr, Bodo Grimbacher, Laura Gamez‑Diaz

Rituximab Monotherapy Is Effective as First-Line Treatment for Granulomatous Lymphocytic Interstitial Lung Disease (GLILD) in CVID Patients

  • Open Access
  • Original Article

Giulio Tessarin, Manuela Baronio, Luisa Gazzurelli, Stefano Rossi, Marco Chiarini, Daniele Moratto, Silvia Clara Giliani, Maria Pia Bondioni, Raffaele Badolato, Vassilios Lougaris

Missed Opportunities to Diagnose Common Variable Immunodeficiency: a Population-Based Case–Control Study Identifying Indicator Diseases for Common Variable Immunodeficiency

  • Open Access
  • Original Article

Christina Dahl, Inge Petersen, Frederik V. Ilkjær, Lena Westh, Terese L. Katzenstein, Ann-Brit E. Hansen, Thyge L. Nielsen, Carsten S. Larsen, Isik S. Johansen, Line D. Rasmussen

Antibody Deficiency in Patients with Biallelic KARS1 Mutations

  • Original Article

Francesco Saettini, Fabiola Guerra, Grazia Fazio, Cristina Bugarin, Hugh J McMillan, Akira Ohtake, Anna Ardissone, Masayuki Itoh, Sabrina Giglio, Gerarda Cappuccio, Giuliana Giardino, Roberta Romano, Manuel Quadri, Serena Gasperini, Daniele Moratto, Marco Chiarini, Ishiguro Akira, Yasuyuki Fukuhara, Itaru Hayakawa, Yasushi Okazaki, Mario Mauri, Rocco Piazza, Gianni Cazzaniga, Andrea Biondi

Correction to: Antibody Deficiency in Patients with Biallelic KARS1 Mutations

  • Author Correction

Francesco Saettini, Fabiola Guerra, Grazia Fazio, Cristina Bugarin, Hugh J. McMillan, Akira Ohtake, Anna Ardissone, Masayuki Itoh, Sabrina Giglio, Gerarda Cappuccio, Giuliana Giardino, Roberta Romano, Manuel Quadri, Serena Gasperini, Daniele Moratto, Marco Chiarini, Akira Ishiguro, Yasuyuki Fukuhara, Itaru Hayakawa, Yasushi Okazaki, Mario Mauri, Rocco Piazza, Gianni Cazzaniga, Andrea Biondi

Effects of Body Mass and Age on the Pharmacokinetics of Subcutaneous or Hyaluronidase-facilitated Subcutaneous Immunoglobulin G in Primary Immunodeficiency Diseases

  • Open Access
  • Original Article

Zhaoyang Li, Kristin Follman, Ed Freshwater, Frank Engler, Leman Yel

Bone Marrow Failure and Immunodeficiency Associated with Human RAD50 Variants

  • Original Article

Masatoshi Takagi, Akihiro Hoshino, Kristine Bousset, Jule Röddecke, Hanna Luisa Martin, Iulia Folcut, Dan Tomomasa, Xi Yang, Junya Kobayashi, Naoki Sakata, Kenichi Yoshida, Satoru Miyano, Seishi Ogawa, Seiji Kojima, Tomohiro Morio, Thilo Dörk, Hirokazu Kanegane

Tocilizumab as a Potential Adjunctive Therapy to Corticosteroids in Cryptococcal Post-infectious Inflammatory Response Syndrome (PIIRS): a Report of Two Cases

  • Original Article

Jessica C. Hargarten, Seher H. Anjum, Kenneth Ssebambulidde, Yoon-Dong Park, Malcolm J. Vaughan, Terri L. Scott, Dima A. Hammoud, Bridgette Jeanne Billioux, Peter R. Williamson

Lung Transplantation under a Janus Kinase Inhibitor in Three Patients with SAVI Syndrome

  • Original Article

Kenza Rhzioual Berrada, Alexandre Belot, Bénédicte Neven, Camille Ohlmann, François Tronc, Gillian Rice, Guillaume Thouvenin, Jean-Christophe Dubus, Julie Mazenq, Marie-Louise Frémond, Nathalie Stremler, Séverine Soummer-Feuillet, Vincent Cottin, Philippe Reix

An Atypical Incontinentia Pigmenti Female with Persistent Mucocutaneous Hyperinflammation and Immunodeficiency Caused by a Novel Germline IKBKG Missense Mutation

  • Original Article

Wenjun Mou, Zhipeng Zhao, Liwei Gao, Libing Fu, Jia Li, Anxia Jiao, Yun Peng, Tong Yu, Yan Guo, Lanqin Chen, Hao Wang, Jun Liu, Qiang Qin, Baoping Xu, Xiuyun Liu, Jianxin He, Jingang Gui

Evaluating Drug Prescription Patterns in Undiagnosed Common Variable Immunodeficiency Patients

  • Original Article

Frederik V. Ilkjær, Isik S. Johansen, Raquel Martin-Iguacel, Lena Westh, Terese L. Katzenstein, Ann-Brit E. Hansen, Thyge L. Nielsen, Carsten S. Larsen, Line D. Rasmussen

A Nationwide Study of GATA2 Deficiency in Italy Reveals Novel Symptoms and Genotype–phenotype Association

  • Original Article

Samuele Roncareggi, Katia Girardi, Francesca Fioredda, Lucia Pedace, Luca Arcuri, Raffaele Badolato, Sonia Bonanomi, Erika Borlenghi, Emilia Cirillo, Tiziana Coliva, Filippo Consonni, Francesca Conti, Piero Farruggia, Eleonora Gambineri, Fabiola Guerra, Franco Locatelli, Gaia Mancuso, Antonio Marzollo, Riccardo Masetti, Concetta Micalizzi, Daniela Onofrillo, Matteo Piccini, Claudio Pignata, Marco Gabriele Raddi, Valeria Santini, Francesca Vendemini, Andrea Biondi, Francesco Saettini

Respiratory Comorbidities Associated with Bronchiectasis in Patients with Common Variable Immunodeficiency in the USIDNET Registry

  • Original Article

Oscar Correa-Jimenez, Sonia Restrepo-Gualteros, Gustavo Nino, Charlotte Cunningham-Rundles, Kathleen E. Sullivan, Ramsay L. Fuleihan, Maria J. Gutierrez

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