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Abdominal Radiology
Erschienen in: Abdominal Radiology 6/2016

23.04.2016

Inherited renal carcinomas

verfasst von: Akira Kawashima, Scott W. Young, Naoki Takahashi, Bernard F. King, Thomas D. Atwell

Erschienen in: Abdominal Radiology | Ausgabe 6/2016

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Abstract

Hereditary forms of kidney carcinoma account for 5–8% of all malignant kidney neoplasms. The renal tumors are often multiple and bilateral and occur at an earlier age. Each of the hereditary kidney carcinoma syndromes is associated with specific gene mutations as well as a specific histologic type of kidney carcinoma. The presence of associated extrarenal manifestations may suggest a hereditary kidney cancer syndrome. Radiology is most commonly used to screen and manage patients with hereditary kidney cancer syndromes. This manuscript reviews the clinical and imaging findings of well-defined inherited kidney cancer syndromes including von Hippel–Lindau disease, Birt–Hogg–Dubé syndrome, hereditary papillary renal carcinoma syndrome, hereditary leiomyomatosis and RCC syndrome, tuberous sclerosis complex, and Lynch syndrome.
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Metadaten
Titel
Inherited renal carcinomas
verfasst von
Akira Kawashima
Scott W. Young
Naoki Takahashi
Bernard F. King
Thomas D. Atwell
Publikationsdatum
23.04.2016
Verlag
Springer US
Erschienen in
Abdominal Radiology / Ausgabe 6/2016
Print ISSN: 2366-004X
Elektronische ISSN: 2366-0058
DOI
https://doi.org/10.1007/s00261-016-0743-6

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