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Erschienen in: Archives of Gynecology and Obstetrics 6/2006

01.10.2006 | Case Report

Pregnancy and C1 esterase inhibitor deficiency: a successful outcome

verfasst von: Fatima Nathani, Helen Sullivan, David Churchill

Erschienen in: Archives of Gynecology and Obstetrics | Ausgabe 6/2006

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Abstract

Hereditary angioedema is a potentially life-threatening condition which can complicate pregnancy. A 34-year-old patient with known C1 esterase inhibitor (C1INH) deficiency was managed successfully in our department and her management was a part of a shared care strategy with the medical and anesthetic departments. Peripartum management plans along with an anesthetic plan were drawn up and clearly displayed in her records. She was admitted three times with abdominal pain which were self-limiting before she was admitted at term. An aggressive management strategy with C1INH concentrate facilitated a normal vaginal delivery.
Literatur
1.
Zurück zum Zitat Agostoni A et al (2004) Hereditary and acquired angioedema: problems and progress: proceedings of the third C1 esterase inhibitor deficiency workshop and beyond. J Allergy Clin Immunol 114(Suppl. 3):S51–S131PubMedCrossRef Agostoni A et al (2004) Hereditary and acquired angioedema: problems and progress: proceedings of the third C1 esterase inhibitor deficiency workshop and beyond. J Allergy Clin Immunol 114(Suppl. 3):S51–S131PubMedCrossRef
2.
Zurück zum Zitat Boulos AN et al (1994) Danazol prophylaxis for delivery in hereditary angioneurotic oedema. Br J Obstet Gynaecol 101(12):1094–1095PubMed Boulos AN et al (1994) Danazol prophylaxis for delivery in hereditary angioneurotic oedema. Br J Obstet Gynaecol 101(12):1094–1095PubMed
3.
Zurück zum Zitat Galan HL et al (1996) Fresh frozen plasma prophylaxis for hereditary angioedema during pregnancy. A case report. J Reprod Med 41(7):541–544 Galan HL et al (1996) Fresh frozen plasma prophylaxis for hereditary angioedema during pregnancy. A case report. J Reprod Med 41(7):541–544
4.
Zurück zum Zitat Jaffe CJ et al (1975) Hereditary angioedema: the use of fresh frozen plasma for prophylaxis in patients undergoing oral surgery. J Allergy Clin Immunol 55(6):386–393PubMedCrossRef Jaffe CJ et al (1975) Hereditary angioedema: the use of fresh frozen plasma for prophylaxis in patients undergoing oral surgery. J Allergy Clin Immunol 55(6):386–393PubMedCrossRef
5.
Zurück zum Zitat Bork K et al (2003) Clinical studies of sudden upper airway obstruction in patients with hereditary angioedema due to C1 esterase inhibitor deficiency. Arch Intern Med 163(10):1229–1235PubMedCrossRef Bork K et al (2003) Clinical studies of sudden upper airway obstruction in patients with hereditary angioedema due to C1 esterase inhibitor deficiency. Arch Intern Med 163(10):1229–1235PubMedCrossRef
6.
Zurück zum Zitat Gompels MM et al (2005) C1 inhibitor deficiency: consensus document. Clin Exp Immunol 139(3):379–394PubMedCrossRef Gompels MM et al (2005) C1 inhibitor deficiency: consensus document. Clin Exp Immunol 139(3):379–394PubMedCrossRef
7.
8.
Zurück zum Zitat Yip J, Cunliffe WJ (1992) Hormonally exacerbated hereditary angioedema. Australas J Dermatol 33(1):35–38PubMedCrossRef Yip J, Cunliffe WJ (1992) Hormonally exacerbated hereditary angioedema. Australas J Dermatol 33(1):35–38PubMedCrossRef
9.
Zurück zum Zitat Lindoff C, Rybo G, Astedt B (1993) Treatment with tranexamic acid during pregnancy, and the risk of thrombo-embolic complications. Thromb Haemost 70(2):238–240PubMed Lindoff C, Rybo G, Astedt B (1993) Treatment with tranexamic acid during pregnancy, and the risk of thrombo-embolic complications. Thromb Haemost 70(2):238–240PubMed
10.
Zurück zum Zitat Logan RA, Greaves MW (1984) Hereditary angio-oedema: treatment with C1 esterase inhibitor concentrate. J R Soc Med 77(12):1046–1048PubMed Logan RA, Greaves MW (1984) Hereditary angio-oedema: treatment with C1 esterase inhibitor concentrate. J R Soc Med 77(12):1046–1048PubMed
11.
Zurück zum Zitat Raychaudhuri K, Buck P, Pumphrey RS (1997) Termination of pregnancy in a patient with hereditary angioedema. Br J Hosp Med 58(6):287–288PubMed Raychaudhuri K, Buck P, Pumphrey RS (1997) Termination of pregnancy in a patient with hereditary angioedema. Br J Hosp Med 58(6):287–288PubMed
12.
Zurück zum Zitat Nielsen EW et al (1996) Hereditary angio-oedema: new clinical observations and autoimmune screening, complement and kallikrein–kinin analyses. J Intern Med 239(2):119–130PubMedCrossRef Nielsen EW et al (1996) Hereditary angio-oedema: new clinical observations and autoimmune screening, complement and kallikrein–kinin analyses. J Intern Med 239(2):119–130PubMedCrossRef
13.
Zurück zum Zitat Halbmayer WM et al (1991) C1-esterase inhibitor in uncomplicated pregnancy and mild and moderate preeclampsia. Thromb Haemost 65(2):134–138PubMed Halbmayer WM et al (1991) C1-esterase inhibitor in uncomplicated pregnancy and mild and moderate preeclampsia. Thromb Haemost 65(2):134–138PubMed
14.
Zurück zum Zitat Postnikoff IM, Pritzker KP (1979) Hereditary angioneurotic edema: an unusual case of maternal mortality. J Forensic Sci 24(2):473–478PubMed Postnikoff IM, Pritzker KP (1979) Hereditary angioneurotic edema: an unusual case of maternal mortality. J Forensic Sci 24(2):473–478PubMed
15.
Zurück zum Zitat Cicardi M et al (1982) Hereditary angioedema: an appraisal of 104 cases. Am J Med Sci 284(1):2–9PubMedCrossRef Cicardi M et al (1982) Hereditary angioedema: an appraisal of 104 cases. Am J Med Sci 284(1):2–9PubMedCrossRef
16.
Zurück zum Zitat Altman AD et al (2006) Hereditary angioedema managed with low-dose danazol and c1 esterase inhibitor concentrate: a case report. J Obstet Gynaecol Can 28(1):27–31PubMed Altman AD et al (2006) Hereditary angioedema managed with low-dose danazol and c1 esterase inhibitor concentrate: a case report. J Obstet Gynaecol Can 28(1):27–31PubMed
17.
Zurück zum Zitat Nalbanski B et al (2002) The rare case of successful pregnancy and delivery in patient with hereditary angioedema. Akush Ginekol (Sofiia) 41(5):39–42 Nalbanski B et al (2002) The rare case of successful pregnancy and delivery in patient with hereditary angioedema. Akush Ginekol (Sofiia) 41(5):39–42
18.
Zurück zum Zitat Hsieh FH, Sheffer AL (2002) Episodic swelling in a pregnant woman from Bangladesh: evaluation and management of angioedema in pregnancy. Allergy Asthma Proc 23(2):157–161PubMed Hsieh FH, Sheffer AL (2002) Episodic swelling in a pregnant woman from Bangladesh: evaluation and management of angioedema in pregnancy. Allergy Asthma Proc 23(2):157–161PubMed
19.
Zurück zum Zitat Ebert A, Pritze W, Weitzel HK (1992) C-1 esterase inhibitor deficiency as an obstetric problem: a case report. Zentralbl Gynakol 114(10):519–522PubMed Ebert A, Pritze W, Weitzel HK (1992) C-1 esterase inhibitor deficiency as an obstetric problem: a case report. Zentralbl Gynakol 114(10):519–522PubMed
20.
Zurück zum Zitat Ferlazzo B et al (1990) Clinical contribution to the problem of correlations between hereditary angioneurotic edema and pregnancy. Minerva Ginecol 42(9):351–356PubMed Ferlazzo B et al (1990) Clinical contribution to the problem of correlations between hereditary angioneurotic edema and pregnancy. Minerva Ginecol 42(9):351–356PubMed
21.
Zurück zum Zitat Bockers M, Bork K (1987) Contraception and pregnancy in hereditary angioedema. Dtsch Med Wochenschr 112(13):507–509PubMedCrossRef Bockers M, Bork K (1987) Contraception and pregnancy in hereditary angioedema. Dtsch Med Wochenschr 112(13):507–509PubMedCrossRef
22.
Zurück zum Zitat Chappatte O, de Swiet M (1988) Hereditary angioneurotic oedema and pregnancy. Case reports and review of the literature. Br J Obstet Gynaecol 95(9):938–942PubMed Chappatte O, de Swiet M (1988) Hereditary angioneurotic oedema and pregnancy. Case reports and review of the literature. Br J Obstet Gynaecol 95(9):938–942PubMed
23.
Zurück zum Zitat Hopkinson RB, Sutcliffe AJ (1979) Hereditary angioneurotic oedema. Anaesthesia 34(2):183–186PubMedCrossRef Hopkinson RB, Sutcliffe AJ (1979) Hereditary angioneurotic oedema. Anaesthesia 34(2):183–186PubMedCrossRef
24.
Zurück zum Zitat McGlinchey PG, Golchin K, McCluskey DR (2000) Life-threatening laryngeal oedema in a pregnant woman with hereditary angioedema. Ulster Med J 69(1):54–57PubMed McGlinchey PG, Golchin K, McCluskey DR (2000) Life-threatening laryngeal oedema in a pregnant woman with hereditary angioedema. Ulster Med J 69(1):54–57PubMed
Metadaten
Titel
Pregnancy and C1 esterase inhibitor deficiency: a successful outcome
verfasst von
Fatima Nathani
Helen Sullivan
David Churchill
Publikationsdatum
01.10.2006
Verlag
Springer-Verlag
Erschienen in
Archives of Gynecology and Obstetrics / Ausgabe 6/2006
Print ISSN: 0932-0067
Elektronische ISSN: 1432-0711
DOI
https://doi.org/10.1007/s00404-006-0183-6

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