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European Archives of Oto-Rhino-Laryngology

Erschienen in:

01.12.2007 | Case Report

Total hearing loss and blindness caused by relapsing polychondritis and myelodysplastic syndrome

verfasst von: Bozena Coha, Ljubica Fustar-Preradovic, Sandra Sekelj, Alen Sekelj

Erschienen in: European Archives of Oto-Rhino-Laryngology | Ausgabe 12/2007

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Abstract

Relapsing polychondritis is an autoimmune disease that primarily manifests as cartilaginous tissue destruction. However, the immune impairment may also involve noncartilaginous tissues such as kidneys, blood vessels, etc. The disease may occur as a primary disorder or in association with other diseases. The case of a female patient with concurrent manifestation of myelodysplastic syndrome—refractory anemia with excess blasts, and relapsing polychondritis, is presented. The diagnosis of relapsing polychondritis was established ten months after the diagnosis of myelodysplastic syndrome, when the criteria for the former were met. Total hearing loss and blindness developed soon thereafter.

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Titel: Total hearing loss and blindness caused by relapsing polychondritis and myelodysplastic syndrome
verfasst von: Bozena Coha
Ljubica Fustar-Preradovic
Sandra Sekelj
Alen Sekelj
Publikationsdatum: 01.12.2007
Verlag: Springer-Verlag
Erschienen in: European Archives of Oto-Rhino-Laryngology / Ausgabe 12/2007
Print ISSN: 0937-4477
Elektronische ISSN: 1434-4726
DOI: https://doi.org/10.1007/s00405-007-0387-9

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Total hearing loss and blindness caused by relapsing polychondritis and myelodysplastic syndrome

Abstract

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Bei schweren Reaktionen auf Insektenstiche empfiehlt sich eine spezifische Immuntherapie

HNO-Op. auch mit über 90?

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Bilateraler Hörsturz hat eine schlechte Prognose

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Springer Medizin

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