Erschienen in:
14.01.2019 | Case Report
Persistent truncus arteriosus with absent semilunar valve in first trimester
verfasst von:
Shui-hua Yang, Xue-qin Li, Zuo-jian Yang, Xiao-xian Tian, Hong-wei Wei
Erschienen in:
Journal of Medical Ultrasonics
|
Ausgabe 2/2019
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Abstract
Persistent truncus arteriosus (PTA) is a relatively uncommon congenital heart disease, accounting for approximately 0.7–1.4% of all congenital cardiac abnormalities worldwide. PTA is usually accompanied by a single semilunar valve, with leaflets ranging from one to six in number. However, absent semilunar valve (ASV) is rarely seen in PTA. Here, we report a case of prenatally diagnosed PTA accompanied by ASV (PTA-ASV) confirmed by postmortem autopsy.