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26.08.2020 | Review Article

Standards of care for Kasabach−Merritt phenomenon in China

verfasst von: Wei Yao, Ke-Lei Li, Zhong-Ping Qin, Kai Li, Jia-Wei Zheng, Xin-Dong Fan, Lin Ma, De-Kai Zhou, Xue-Jian Liu, Li Wei, Li Li, Mao-Zhong Tai, Jin-Hu Wang, Yi Ji, Lin Zhou, Hai-Jin Huang, Xiao-Yun Gao, Zhi-Jian Huang, Song Gu, He-Ying Yang

Erschienen in: World Journal of Pediatrics | Ausgabe 2/2021

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Abstract

Kasabach−Merritt phenomenon (KMP) is a rare disease that is characterized by severe thrombocytopenia and consumptive coagulation dysfunction caused by kaposiform hemangioendothelioma or tufted hemangioma. This condition primarily occurs in infants and young children, usually with acute onset and rapid progression. This review article introduced standardized recommendations for the pathogenesis, clinical manifestation, diagnostic methods and treatment process of KMP in China, which can be used as a reference for clinical practice.

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Titel: Standards of care for Kasabach−Merritt phenomenon in China
verfasst von: Wei Yao
Ke-Lei Li
Zhong-Ping Qin
Kai Li
Jia-Wei Zheng
Xin-Dong Fan
Lin Ma
De-Kai Zhou
Xue-Jian Liu
Li Wei
Li Li
Mao-Zhong Tai
Jin-Hu Wang
Yi Ji
Lin Zhou
Hai-Jin Huang
Xiao-Yun Gao
Zhi-Jian Huang
Song Gu
He-Ying Yang
Publikationsdatum: 26.08.2020
Verlag: Springer Singapore
Erschienen in: World Journal of Pediatrics / Ausgabe 2/2021
Print ISSN: 1708-8569
Elektronische ISSN: 1867-0687
DOI: https://doi.org/10.1007/s12519-020-00379-9

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Standards of care for Kasabach−Merritt phenomenon in China

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