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Clinical Rheumatology

Erschienen in:

14.03.2016 | Review Article

Rheumatologic manifestations of primary immunodeficiency diseases

verfasst von: V. R. Dimitriades, R. Sorensen

Erschienen in: Clinical Rheumatology | Ausgabe 4/2016

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Abstract

In the last 5 years, several hundred articles have been published concerning the link between primary immunodeficiency disease (PID) and rheumatologic diseases. Although rheumatologic complications were originally thought to be at the opposite ends of the spectrum of immunopathologic manifestations, they are now all being considered secondary manifestations of a causative primary “immune derangement.” For the rheumatologist, it is important to be able to identify patients who may present with typical rheumatologic findings but who have an underlying PID. In a systematic manner, this overview addresses both the systemic and organ-based rheumatologic diseases which have known associations with primary immunodeficiencies, and explores how immunodeficiency may actually cause these clinical manifestations.

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Titel: Rheumatologic manifestations of primary immunodeficiency diseases
verfasst von: V. R. Dimitriades
R. Sorensen
Publikationsdatum: 14.03.2016
Verlag: Springer London
Erschienen in: Clinical Rheumatology / Ausgabe 4/2016
Print ISSN: 0770-3198
Elektronische ISSN: 1434-9949
DOI: https://doi.org/10.1007/s10067-016-3229-6

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