Erschienen in:
01.04.2003 | Laboratory Investigations
Angiography of Hepatic Vascular Malformations Associated with
Hereditary Hemorrhagic Telangiectasia
verfasst von:
Manabu Hashimoto, Etuko Tate, Toshiaki Nishii, Jiro Watarai, Takanobu Shioya, Robert I. White
Erschienen in:
CardioVascular and Interventional Radiology
|
Ausgabe 2/2003
Einloggen, um Zugang zu erhalten
Abstract
Purpose: To describe the angiographic
features of hepatic involvement in hereditary hemorrhagic
telangiectasia (HHT), particularly the presence of portovenous
shunts.
Methods: We reviewed the angiographic findings
of seven patients with HHT. The patients comprised three women and four
men with a mean age of 51 years.
Results: Intrahepatic
telangiectasias were found in all seven patients and shunts between
three vascular channels were found in six of seven patients. In the
four patients who had portovenous shunts combined with arterioportal
shunts, the portovenous shunts were large. Three patients had no
portovenous shunts. Two of these patients had arteriovenous shunts, and
one had no shunt. The mean age (69 years) of the patients with
portovenous shunts was older than those without portovenous shunts (26
years).
Conclusions: Hepatic vascular lesions in HHT are
varied, ranging from telangiectasias to large shunts between three
vascular channels. In an advanced stage of involvement, large
portovenous shunts are present.