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01.03.2013

Intraductal Polypoid Lipid-Rich Neuroendocrine Tumor of the Pancreas with Entrapped Ductules: Case Report and Review of the Literature

verfasst von: Jaclyn Frances Hechtman, Bernardo Franssen, Daniel M. Labow, Ronald E. Gordon, Christopher J. DiMaio, Eric J. Wilck, Gonzalo Carrasco-Avino, Hongfa Zhu

Erschienen in: Endocrine Pathology | Ausgabe 1/2013

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Abstract

Pancreatic neuroendocrine tumors of the main pancreatic duct are rare and usually small due to symptoms of pancreatic duct obstruction. We present a case of a large (3 cm), well-differentiated (G1) lipid-rich polypoid neuroendocrine tumor of the pancreas completely occluding the main pancreatic duct with non-neoplastic-entrapped ductules and CK19 positivity. Clinical, radiological, gross, microscopic, immunohistochemical, and ultrastructural findings are discussed. The literature pertaining to the unique features of this case is reviewed including clinical and pathologic pitfalls and the possible etiologic and prognostic significance of these findings.

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Titel: Intraductal Polypoid Lipid-Rich Neuroendocrine Tumor of the Pancreas with Entrapped Ductules: Case Report and Review of the Literature
verfasst von: Jaclyn Frances Hechtman
Bernardo Franssen
Daniel M. Labow
Ronald E. Gordon
Christopher J. DiMaio
Eric J. Wilck
Gonzalo Carrasco-Avino
Hongfa Zhu
Publikationsdatum: 01.03.2013
Verlag: Springer US
Erschienen in: Endocrine Pathology / Ausgabe 1/2013
Print ISSN: 1046-3976
Elektronische ISSN: 1559-0097
DOI: https://doi.org/10.1007/s12022-012-9231-x

Springer Medizin

Intraductal Polypoid Lipid-Rich Neuroendocrine Tumor of the Pancreas with Entrapped Ductules: Case Report and Review of the Literature

Abstract

Neu im Fachgebiet Pathologie

Molekularpathologische Untersuchungen im Wandel der Zeit

Vergleichende Pathologie in der onkologischen Forschung

Gastrointestinale Stromatumoren

Personalisierte Medizin in der Onkologie

Springer Medizin

Abstract

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