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Erschienen in: European Journal of Pediatrics 8/2004

01.08.2004 | Original Paper

Management of stage I cervical sarcoma botryoides in childhood and adolescence

verfasst von: Susanne E. M. Gruessner, Charles O. A. Omwandho, Thomas Dreyer, Renate Blütters-Sawatzki, Alfred Reiter, Hans R. Tinneberg, Rainer M. Bohle

Erschienen in: European Journal of Pediatrics | Ausgabe 8/2004

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Abstract

Rhabdomyosarcomas are the most common soft tissue sarcomas in childhood. The botryoid variant arises in infancy from the vagina or urinary bladder and extremely rarely from the uterine cervix. Treatment regimes range from local excision of the tumour to radical hysterectomy with adjuvant multidrug therapy and/or radiotherapy. In cases of minimal cervical invasion, the less invasive local excision in combination with adjuvant chemotherapy has resulted in excellent survival rates with complete functional preservation of the bladder, rectum, vagina, and ovaries. We present here a 30-year literature review and a case report of a cervical sarcoma botryoides in a 5-year-old girl. Conclusion:based on the literature review and our own observation, we recommend minor surgical approaches in combination with chemotherapy as the treatment of choice for early stage I cervical rhabdomyosarcoma.
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Metadaten
Titel
Management of stage I cervical sarcoma botryoides in childhood and adolescence
verfasst von
Susanne E. M. Gruessner
Charles O. A. Omwandho
Thomas Dreyer
Renate Blütters-Sawatzki
Alfred Reiter
Hans R. Tinneberg
Rainer M. Bohle
Publikationsdatum
01.08.2004
Verlag
Springer-Verlag
Erschienen in
European Journal of Pediatrics / Ausgabe 8/2004
Print ISSN: 0340-6199
Elektronische ISSN: 1432-1076
DOI
https://doi.org/10.1007/s00431-004-1469-y

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