The online version of this article (doi:10.1186/1477-7819-10-279) contains supplementary material, which is available to authorized users.
The authors declare that they have no competing interests.
CS drafted the manuscript. SJ and JL did the operation for the patient. KX and WD collected the materials. ZD provided the pathological figures. All authors read and approved the final manuscript.
Renal primitive neuroectodermal tumor (rPNET) as a member of Ewing’s sarcoma family is extremely rare and usually occurs in children and young adults. Most literature about rPNET was isolated case reports.
We reported a case of 45-year-old man with the complaint of right flank pain. Computerized tomography (CT) scan demonstrated a large substantive tumor involving the lower pole of the right kidney. Then the patient underwent radical nephrectomy. Pathologic characteristics and immunohistochemical analysis confirmed the diagnosis of rPNET. Additionally, the patient received three cycles of chemotherapy, and was still alive without metastasis at 15-months follow-up.
rPNET is rare and presents aggressive clinical behavior and worse prognosis. We expect that further awareness and study of this rare tumor can be had by presenting our case.
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- Primitive neuroectodermal tumor of the kidney: case report and review of literature
- BioMed Central
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