Erschienen in:
01.09.2007 | Case Discussion
Successful use of extracorporeal membrane oxygenation for severe interstitial lung disease in a child with dermatomyositis
verfasst von:
Francesco Zulian, Maria Martha Martinez Toledo, Angela Amigoni, Giorgia Martini, Caterina Agosto, Andrea Pettenazzo
Erschienen in:
Intensive Care Medicine
|
Ausgabe 9/2007
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Excerpt
Juvenile dermatomyositis (JDM) is a multisystemic disease of children that affects primarily muscle and skin. The prevalence of pulmonary involvement is not well known but seems to be rarer than in adult patients with dermatomyositis/polymyositis (DM/PM) [
1‐
3]. A wide spectrum of clinical presentations have been described, ranging from asymptomatic patients with merely abnormal pulmonary function tests [
4] to severe, potentially fatal cases refractory to immunosuppressive and supportive therapy [
5-
9]. Here we present the case of a child with JDM and severe interstitial lung disease (ILD) successfully treated with immunosuppressive drugs and extracorporeal membrane oxygenation (ECMO). …